[Diagnostic approach of pheochromocytomas and paragangliomas].

Enfoque diagnóstico de feocromocitomas y paragangliomas.

Journal

Hipertension y riesgo vascular
ISSN: 1989-4805
Titre abrégé: Hipertens Riesgo Vasc
Pays: Spain
ID NLM: 101510649

Informations de publication

Date de publication:
Historique:
received: 27 06 2018
accepted: 30 06 2018
pubmed: 7 8 2018
medline: 18 12 2019
entrez: 7 8 2018
Statut: ppublish

Résumé

Pheochromocytomas and paragangliomas are rare neuroendocrine tumours associated with high morbidity and mortality. Recognizing the clinical presentation is the first step for diagnosis. Biochemical studies may determine an excess of catecholamines and their metabolites. However, the available tests offer varying diagnosis precision. Computed tomography and magnetic resonance are highly sensitive for locating these tumours. Functional tests are reserved for when metastatic and multifocal disease are suspected. One third of the patients have a germline mutation and many genes are involved in the development of these tumours.

Identifiants

pubmed: 30078655
pii: S1889-1837(18)30089-8
doi: 10.1016/j.hipert.2018.06.003
pii:
doi:

Types de publication

Journal Article

Langues

spa

Sous-ensembles de citation

IM

Pagination

34-43

Informations de copyright

Copyright © 2018 SEH-LELHA. Publicado por Elsevier España, S.L.U. All rights reserved.

Auteurs

R M Gómez (RM)

Hospital de Clínicas, Ciudad Autónoma de Buenos Aires, Argentina. Electronic address: valeria.demiguel@hospitalitaliano.org.ar.

M Hernaiz (M)

Hospital de Clínicas, Ciudad Autónoma de Buenos Aires, Argentina.

V de Miguel (V)

Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina.

L S Aparicio (LS)

Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina.

M J Marín (MJ)

Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina.

S Lupi (S)

Hospital Ramos Mejía, Ciudad Autónoma de Buenos Aires, Argentina.

M Barontini (M)

CEDIE, Hospital de Niños Ricardo Gutiérrez, Ciudad Autónoma de Buenos Aires, Argentina.

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Classifications MeSH