Metastatic Phaeochromocytoma: Spinning Towards More Promising Treatment Options.
Journal
Experimental and clinical endocrinology & diabetes : official journal, German Society of Endocrinology [and] German Diabetes Association
ISSN: 1439-3646
Titre abrégé: Exp Clin Endocrinol Diabetes
Pays: Germany
ID NLM: 9505926
Informations de publication
Date de publication:
Feb 2019
Feb 2019
Historique:
pubmed:
21
9
2018
medline:
1
6
2019
entrez:
21
9
2018
Statut:
ppublish
Résumé
Phaeochromocytomas (PCC) and paragangliomas (PGL) are rare tumours arising from the chromaffin cells of the adrenal medulla (PCC) or the paraganglia located outside the adrenal gland (PGL). However, their incidence is likely to be underestimated; around 10% of all PCC/PGL are metastatic, with higher metastatic potential of PGLs compared to PCCs. If benign, surgery is the treatment of choice, but if metastatic, therapy is challenging. Here we review the currently existing therapy options for metastatic PCCs/PGLs including conventional chemotherapy (the original Averbuch scheme, but updated), radiopharmaceutical treatments (
Identifiants
pubmed: 30235495
doi: 10.1055/a-0715-1888
pmc: PMC7443617
mid: NIHMS1619673
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
117-128Subventions
Organisme : Intramural NIH HHS
ID : Z99 HD999999
Pays : United States
Informations de copyright
© Georg Thieme Verlag KG Stuttgart · New York.
Déclaration de conflit d'intérêts
No conflict of interest has been declared by the authors.
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