Differences in clinical features of acute exacerbation between connective tissue disease-associated interstitial pneumonia and idiopathic pulmonary fibrosis.
Aged
Aged, 80 and over
Biopsy
Connective Tissue Diseases
/ complications
Diagnosis, Differential
Disease Management
Disease Progression
Female
Forced Expiratory Volume
/ physiology
Humans
Idiopathic Pulmonary Fibrosis
/ diagnosis
Lung Diseases, Interstitial
/ diagnosis
Male
Middle Aged
Prognosis
Recurrence
Retrospective Studies
Tomography, X-Ray Computed
/ methods
Connective tissue disease
acute exacerbation
idiopathic pulmonary fibrosis
interstitial pneumonia
rheumatoid arthritis
Journal
Chronic respiratory disease
ISSN: 1479-9731
Titre abrégé: Chron Respir Dis
Pays: England
ID NLM: 101197408
Informations de publication
Date de publication:
Historique:
pubmed:
2
11
2018
medline:
9
6
2020
entrez:
2
11
2018
Statut:
ppublish
Résumé
Acute exacerbation of idiopathic pulmonary fibrosis (AE-IPF) is a devastating condition that frequently occurs in the advanced stage of IPF. However, the clinical features in AE of connective tissue disease-associated interstitial pneumonia (AE-CTD-IP) have not been well-established. The aim of this study was to clarify the clinical features of AE-CTD-IP and to compare them with those of AE-IPF. Fifteen AE-CTD-IP patients and 48 AE-IPF patients who were diagnosed and treated at our hospital were retrospectively studied. Compared with AE-IPF patients, AE-CTD-IP patients had a significantly higher %FVC (median, 94.8 vs. 56.3%; p < 0.001) and a lower extent of honeycombing on HRCT ( p = 0.020) within 1 year before AE. At AE, AE-CTD-IP patients showed higher white blood cell counts (12.0 vs. 9.9 × 10
Identifiants
pubmed: 30380910
doi: 10.1177/1479972318809476
pmc: PMC6301840
doi:
Types de publication
Comparative Study
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
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