Primary idiopathic CNS non-amyloidogenic light chain deposition disease complicated by treatment-resistant focal seizure disorder.
Journal
Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
ISSN: 1532-2653
Titre abrégé: J Clin Neurosci
Pays: Scotland
ID NLM: 9433352
Informations de publication
Date de publication:
Jan 2019
Jan 2019
Historique:
received:
18
06
2018
accepted:
27
10
2018
pubmed:
15
11
2018
medline:
13
2
2019
entrez:
15
11
2018
Statut:
ppublish
Résumé
Light chain deposition disease (LCDD) is a systemic disorder characterised by the pathologic deposition of immunoglobulin light chains, which is histologically distinguished from amyloidosis by failure to stain with Congo red. Central nervous system (CNS)-restricted LCDD is among the rarest manifestations. We describe a unique case complicated by focal onset epilepsy with impaired awareness for which control with anticonvulsant therapy proved difficult.
Identifiants
pubmed: 30424969
pii: S0967-5868(18)31065-8
doi: 10.1016/j.jocn.2018.10.123
pii:
doi:
Substances chimiques
Immunoglobulin Light Chains
0
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
313-315Informations de copyright
Copyright © 2018 Elsevier Ltd. All rights reserved.