Prevalence and correlates of growth failure in young African patients with sickle cell disease.


Journal

British journal of haematology
ISSN: 1365-2141
Titre abrégé: Br J Haematol
Pays: England
ID NLM: 0372544

Informations de publication

Date de publication:
01 2019
Historique:
received: 22 05 2018
accepted: 06 09 2018
pubmed: 24 11 2018
medline: 19 9 2019
entrez: 24 11 2018
Statut: ppublish

Résumé

Growth failure (GF) in children with sickle cell disease (SCD) tends to decline in high-income countries, but data are lacking in sub-Saharan Africa. We performed a cross-sectional study nested in the CADRE (Cœur, Artères et DREpanocytose) cohort in Mali, Senegal, Cameroon, Gabon and the Ivory Coast. SCD patients and healthy controls aged 5-21 years old were recruited (n = 2583). Frequency of GF, defined as a height, weight or body mass index below the 5th percentile on World health Organization growth charts, was calculated. We assessed associations between GF and SCD phenotypic group, clinical and biological characteristics and history of SCD-related complications. GF was diagnosed in 51% of HbSS, 58% of HbSβ

Identifiants

pubmed: 30467843
doi: 10.1111/bjh.15638
doi:

Substances chimiques

Hemoglobin, Sickle 0

Types de publication

Clinical Trial Journal Article Multicenter Study Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

253-262

Informations de copyright

© 2018 British Society for Haematology and John Wiley & Sons Ltd.

Auteurs

Laure Alexandre-Heymann (L)

Internal Medicine Unit, Hôpital Européen Georges Pompidou, Assistance Publique des Hôpitaux de Paris, Paris, France.

Marie Dubert (M)

Internal Medicine Unit, Hôpital Européen Georges Pompidou, Assistance Publique des Hôpitaux de Paris, Paris, France.
UMR_S970, Université Paris Descartes, Inserm, Paris, France.

Dapa A Diallo (DA)

Centre de Recherche et Lutte contre la Drépanocytose, Bamako, Mali.

Saliou Diop (S)

Centre National de Transfusion Sanguine, Dakar, Senegal.

Aissata Tolo (A)

Haematology Unit, CHU de Yopougon, Abidjan, Ivory Coast.

Suzanne Belinga (S)

Centre Pasteur du Cameroun, Yaoundé, Cameroon.

Ibrahima Sanogo (I)

Haematology Unit, CHU de Yopougon, Abidjan, Ivory Coast.

Ibrahima Diagne (I)

Pediatrics Unit, CHU de Fann, Dakar, Senegal.

Guillaume Wamba (G)

Pediatrics Unit, Centre Hospitalier d'Essos, Yaoundé, Cameroon.

Kouakou Boidy (K)

Centre National de Transfusion Sanguine, Dakar, Senegal.

Indou Deme Ly (ID)

Pediatrics Unit, CHU de Fann, Dakar, Senegal.

Ismaël Kamara (I)

Centre National de Transfusion Sanguine, Dakar, Senegal.

Youssouf Traore (Y)

UMR_S970, Université Paris Descartes, Inserm, Paris, France.

Lucile Offredo (L)

UMR_S970, Université Paris Descartes, Inserm, Paris, France.

Xavier Jouven (X)

UMR_S970, Université Paris Descartes, Inserm, Paris, France.
Cardiology Unit, Hôpital Européen Georges Pompidou, Assistance Publique des Hôpitaux de Paris, Paris, France.

Brigitte Ranque (B)

Internal Medicine Unit, Hôpital Européen Georges Pompidou, Assistance Publique des Hôpitaux de Paris, Paris, France.
UMR_S970, Université Paris Descartes, Inserm, Paris, France.

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Classifications MeSH