Early-onset colorectal cancer in young individuals.
colorectal cancer
familial colorectal cancer
hereditary colorectal cancer
sporadic early-onset colorectal cancer
young adults
Journal
Molecular oncology
ISSN: 1878-0261
Titre abrégé: Mol Oncol
Pays: United States
ID NLM: 101308230
Informations de publication
Date de publication:
02 2019
02 2019
Historique:
received:
04
09
2018
revised:
01
11
2018
accepted:
20
11
2018
pubmed:
7
12
2018
medline:
18
12
2019
entrez:
7
12
2018
Statut:
ppublish
Résumé
Treatment of young adults with colorectal cancer (CRC) represents an unmet clinical need, especially as diagnosis in this population might lead to the greatest loss of years of life. Since 1994, CRC incidence in individuals younger than 50 years has been increasing by 2% per year. The surge in CRC incidence in young adults is particularly alarming as the overall CRC frequency has been decreasing. Early-onset CRC are characterized by a more advanced stage at diagnosis, poorer cell differentiation, higher prevalence of signet ring cell histology, and left colon-sided location of the primary tumor. Among EO-CRC, approximately 30% of patients are affected by tumors harboring mutations causing hereditary cancer predisposing syndromes, and 20% have familial CRC. Most notably, the remaining 50% of EO-CRC patients have neither hereditary syndromes nor familial CRC, thus representing a formidable challenge for research. In this review article we summarize epidemiology, clinical and molecular features, heredity and outcome of treatments of EO-CRC, and provide considerations for future perspectives.
Identifiants
pubmed: 30520562
doi: 10.1002/1878-0261.12417
pmc: PMC6360363
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
109-131Informations de copyright
© 2018 The Authors. Published by FEBS Press and John Wiley & Sons Ltd.
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