Technical Considerations for Lung Transplantation in Kartagener's Syndrome.
Journal
The Annals of thoracic surgery
ISSN: 1552-6259
Titre abrégé: Ann Thorac Surg
Pays: Netherlands
ID NLM: 15030100R
Informations de publication
Date de publication:
05 2019
05 2019
Historique:
received:
20
07
2018
revised:
29
08
2018
accepted:
30
08
2018
pubmed:
8
1
2019
medline:
20
12
2019
entrez:
8
1
2019
Statut:
ppublish
Résumé
Kartagener's syndrome is a rare genetic disorder of ciliated epithelial cells associated with recurrent respiratory tract infections, bronchiectasis, and situs inversus. In some patients, the accumulation of airway secretions and recurrent infections lead to end-stage lung disease, for which lung transplantation is the only effective treatment. Anatomical variations, such as dextrocardia and pulmonary situs inversus, make the procedure challenging, yet feasible with certain technical modifications and careful preparation of donor lungs. We report a case of bilateral lung transplantation without the use of cardiopulmonary bypass in a patient with Kartagener's syndrome while describing important technical details of the operation.
Identifiants
pubmed: 30612988
pii: S0003-4975(18)31528-5
doi: 10.1016/j.athoracsur.2018.08.095
pii:
doi:
Types de publication
Case Reports
Journal Article
Research Support, N.I.H., Extramural
Langues
eng
Sous-ensembles de citation
IM
Pagination
e337-e339Subventions
Organisme : NHLBI NIH HHS
ID : F32 HL143950
Pays : United States
Organisme : NCI NIH HHS
ID : K07 CA178120
Pays : United States
Informations de copyright
Copyright © 2019 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved.