Leptomeningeal Gliomatosis: A Single Institution Study of 31 Patients.


Journal

Anticancer research
ISSN: 1791-7530
Titre abrégé: Anticancer Res
Pays: Greece
ID NLM: 8102988

Informations de publication

Date de publication:
Feb 2019
Historique:
received: 05 12 2018
revised: 27 12 2018
accepted: 03 01 2019
entrez: 4 2 2019
pubmed: 4 2 2019
medline: 21 3 2019
Statut: ppublish

Résumé

Secondary leptomeningeal gliomatosis (LG) is a rare and severe progression pattern of glioma. Our objective was to evaluate the characteristics and outcome of patients with LG. We retrospectively reviewed 31 patients diagnosed with secondary LG. At the time of LG diagnosis, the median age of patients was 45 years. The histological grade was IV in 20 patients and II to III in 11 patients. As a first-line of therapy for LG, 22 patients received an oncological treatment: i) BCNU-temozolomide (TMZ) (n=15), ii) other type of chemotherapy (n=7), and iii) no treatment (supportive care) (n=9). Following LG diagnosis, the median progression-free survival (PFS) and overall survival (OS) were 1.8 months [95% confidence interval (CI)=0.9-2.7] and 2.1 months (95%CI=1.3-3), respectively. The univariate analyses showed an improved OS with age of less than 45 years (p<0.001), a prolonged interval from the initial glioma diagnosis (IGD) to LG diagnosis (p=0.003), BCNU-TMZ as the preferred first-line treatment for LG out of the three options (p=0.008), and Karnofsky performance status (KPS) ≥70 (p=0.012). Prolonged interval from IGD to LG diagnosis (HR=5.839) and BCNU-TMZ as the chosen first-line treatment for LG (HR=6.635) remained significant in the multivariate analyses as well. Among the 22 treated patients, the median OS was significantly higher (p=0.008) with the BCNU-TMZ treatment (5.7 months; 95%CI=4.2-7.1), compared to other types of treatment offered (2 months; 95%CI=1.1-2.9). The time interval from the IGD to the LG diagnosis is a potential prognostic factor for LG. BCNU-TMZ may be a therapeutic option in the present setting.

Sections du résumé

BACKGROUND/AIM OBJECTIVE
Secondary leptomeningeal gliomatosis (LG) is a rare and severe progression pattern of glioma. Our objective was to evaluate the characteristics and outcome of patients with LG.
PATIENTS AND METHODS METHODS
We retrospectively reviewed 31 patients diagnosed with secondary LG. At the time of LG diagnosis, the median age of patients was 45 years. The histological grade was IV in 20 patients and II to III in 11 patients. As a first-line of therapy for LG, 22 patients received an oncological treatment: i) BCNU-temozolomide (TMZ) (n=15), ii) other type of chemotherapy (n=7), and iii) no treatment (supportive care) (n=9).
RESULTS RESULTS
Following LG diagnosis, the median progression-free survival (PFS) and overall survival (OS) were 1.8 months [95% confidence interval (CI)=0.9-2.7] and 2.1 months (95%CI=1.3-3), respectively. The univariate analyses showed an improved OS with age of less than 45 years (p<0.001), a prolonged interval from the initial glioma diagnosis (IGD) to LG diagnosis (p=0.003), BCNU-TMZ as the preferred first-line treatment for LG out of the three options (p=0.008), and Karnofsky performance status (KPS) ≥70 (p=0.012). Prolonged interval from IGD to LG diagnosis (HR=5.839) and BCNU-TMZ as the chosen first-line treatment for LG (HR=6.635) remained significant in the multivariate analyses as well. Among the 22 treated patients, the median OS was significantly higher (p=0.008) with the BCNU-TMZ treatment (5.7 months; 95%CI=4.2-7.1), compared to other types of treatment offered (2 months; 95%CI=1.1-2.9).
CONCLUSION CONCLUSIONS
The time interval from the IGD to the LG diagnosis is a potential prognostic factor for LG. BCNU-TMZ may be a therapeutic option in the present setting.

Identifiants

pubmed: 30711992
pii: 39/2/1035
doi: 10.21873/anticanres.13210
doi:

Substances chimiques

Carmustine U68WG3173Y
Temozolomide YF1K15M17Y

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

1035-1041

Informations de copyright

Copyright© 2019, International Institute of Anticancer Research (Dr. George J. Delinasios), All rights reserved.

Auteurs

Didier Autran (D)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France didier.autran@ap-hm.fr.

Maryline Barrie (M)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.

Mona Matta (M)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.

Colette Monserrat (C)

Laboratory of Biochemistry, AP-HM, CHU Timone, Marseille, France.

Chantal Campello (C)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.

Gregorio Petrirena (G)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.

Celine Boucard (C)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.

Laetitia Padovani (L)

Department of Radiotherapy, AP-HM, CHU Timone, Marseille, France.

Anderson Loundou (A)

EA 3279, Aix-Marseille University, Marseille, France.

Romain Appay (R)

Department of Anatomopathology-Neuropathology, AP-HM, CHU Timone, Marseille, France.

Thomas Graillon (T)

Department of Neuro-Surgery, AP-HM, CHU Timone, Marseille, France.

Henry Dufour (H)

Department of Neuro-Surgery, AP-HM, CHU Timone, Marseille, France.

Dominique Figarella-Branger (D)

Department of Anatomopathology-Neuropathology, AP-HM, CHU Timone, Marseille, France.
UMR7051, INP, Team 8, Aix-Marseille University, Marseille, France.

Olivier Chinot (O)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.
UMR7051, INP, Team 8, Aix-Marseille University, Marseille, France.

Emeline Tabouret (E)

Department of Neuro-Oncology, AP-HM, CHU Timone, Marseille, France.
UMR7051, INP, Team 8, Aix-Marseille University, Marseille, France.

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