Folliculin regulates mTORC1/2 and WNT pathways in early human pluripotency.


Journal

Nature communications
ISSN: 2041-1723
Titre abrégé: Nat Commun
Pays: England
ID NLM: 101528555

Informations de publication

Date de publication:
07 02 2019
Historique:
received: 22 06 2017
accepted: 05 12 2018
entrez: 9 2 2019
pubmed: 9 2 2019
medline: 9 4 2019
Statut: epublish

Résumé

To reveal how cells exit human pluripotency, we designed a CRISPR-Cas9 screen exploiting the metabolic and epigenetic differences between naïve and primed pluripotent cells. We identify the tumor suppressor, Folliculin(FLCN) as a critical gene required for the exit from human pluripotency. Here we show that FLCN Knock-out (KO) hESCs maintain the naïve pluripotent state but cannot exit the state since the critical transcription factor TFE3 remains active in the nucleus. TFE3 targets up-regulated in FLCN KO exit assay are members of Wnt pathway and ESRRB. Treatment of FLCN KO hESC with a Wnt inhibitor, but not ESRRB/FLCN double mutant, rescues the cells, allowing the exit from the naïve state. Using co-immunoprecipitation and mass spectrometry analysis we identify unique FLCN binding partners. The interactions of FLCN with components of the mTOR pathway (mTORC1 and mTORC2) reveal a mechanism of FLCN function during exit from naïve pluripotency.

Identifiants

pubmed: 30733432
doi: 10.1038/s41467-018-08020-0
pii: 10.1038/s41467-018-08020-0
pmc: PMC6367455
doi:

Substances chimiques

Basic Helix-Loop-Helix Leucine Zipper Transcription Factors 0
ESRRB protein, human 0
Receptors, Estrogen 0
TFE3 protein, human 0
Estrone 2DI9HA706A
Mechanistic Target of Rapamycin Complex 1 EC 2.7.11.1
Mechanistic Target of Rapamycin Complex 2 EC 2.7.11.1

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

632

Subventions

Organisme : NIGMS NIH HHS
ID : P01 GM081619
Pays : United States
Organisme : NHLBI NIH HHS
ID : U01 HL099997
Pays : United States
Organisme : NIGMS NIH HHS
ID : R01 GM083867
Pays : United States
Organisme : NHLBI NIH HHS
ID : U01 HL099993
Pays : United States
Organisme : NIGMS NIH HHS
ID : R01 GM097372
Pays : United States
Organisme : NIDDK NIH HHS
ID : P30 DK017047
Pays : United States

Références

Stem Cell Reports. 2014 Mar 06;2(3):366-81
pubmed: 24672758
Dev Cell. 2015 Nov 9;35(3):366-82
pubmed: 26555056
Cell Stem Cell. 2013 Dec 5;13(6):663-75
pubmed: 24315441
Cell Stem Cell. 2016 Mar 3;18(3):323-329
pubmed: 26853856
Nat Chem Biol. 2013 May;9(5):300-6
pubmed: 23455543
Mol Med. 2012 May 09;18:423-32
pubmed: 22193356
Nat Cell Biol. 2011 Aug 14;13(9):1070-5
pubmed: 21841791
J Cell Biol. 2013 Sep 30;202(7):1107-22
pubmed: 24081491
Bioinformatics. 2015 Jan 15;31(2):166-9
pubmed: 25260700
Nat Struct Mol Biol. 2013 Sep;20(9):1131-9
pubmed: 23934149
Nucleic Acids Res. 2016 Jan 4;44(D1):D447-56
pubmed: 26527722
PLoS One. 2010 Dec 29;5(12):e15793
pubmed: 21209915
Nature. 2013 Dec 12;504(7479):282-6
pubmed: 24172903
Nature. 2010 Nov 11;468(7321):316-20
pubmed: 20953172
Nat Commun. 2017 Jun 28;8:15866
pubmed: 28656962
Stem Cells. 2014 May;32(5):1230-8
pubmed: 24497442
F1000Res. 2014 Apr 24;3:95
pubmed: 24860646
Development. 2015 Sep 15;142(18):3090-9
pubmed: 26395138
Biostatistics. 2007 Jan;8(1):118-27
pubmed: 16632515
Nat Rev Urol. 2015 Oct;12(10):558-69
pubmed: 26334087
Genome Biol. 2009;10(3):R25
pubmed: 19261174
Science. 2014 Jun 6;344(6188):1156-1160
pubmed: 24904165
Cell Stem Cell. 2012 Oct 5;11(4):477-90
pubmed: 23040477
Nature. 2016 Sep 1;537(7618):57-62
pubmed: 27556940
Proc Natl Acad Sci U S A. 2014 Mar 25;111(12):4484-9
pubmed: 24623855
EMBO J. 2013 Oct 2;32(19):2548-60
pubmed: 23942238
Cell Stem Cell. 2012 Oct 5;11(4):491-504
pubmed: 23040478
FEBS Lett. 2013 Sep 17;587(18):2924-9
pubmed: 23892082
J Biol Chem. 2017 Mar 17;292(11):4743-4752
pubmed: 28174303
Science. 2014 Jan 3;343(6166):84-87
pubmed: 24336571
Cell Rep. 2018 Jul 10;24(2):489-502
pubmed: 29996108
Genes Dev. 2016 Nov 15;30(22):2551-2564
pubmed: 27913603
J Natl Compr Canc Netw. 2016 Jan;14(1):8-17
pubmed: 26733551
Methods Enzymol. 1993;225:803-23
pubmed: 8231888
Nat Cell Biol. 2015 Dec;17(12):1519-21
pubmed: 26612574
Cell Cycle. 2018;17(5):535-549
pubmed: 29466914
Alcohol. 1998 May;15(4):305-9
pubmed: 9590515
Nature. 2007 Jul 12;448(7150):196-9
pubmed: 17597760
Stem Cells. 2016 Apr;34(4):1068-82
pubmed: 27095138
Cell Stem Cell. 2016 Oct 6;19(4):502-515
pubmed: 27424783
Cell. 2013 Apr 11;153(2):335-47
pubmed: 23582324
Cell. 2014 Sep 11;158(6):1254-1269
pubmed: 25215486
Oncogene. 2006 Sep 28;25(44):5933-41
pubmed: 16636660
Cell Metab. 2017 May 2;25(5):1103-1117.e6
pubmed: 28467928
J Pharmacol Exp Ther. 1997 Sep;282(3):1305-11
pubmed: 9316839
Open Biol. 2012 Aug;2(8):120071
pubmed: 22977732
Cell Rep. 2016 Mar 15;14(10):2301-12
pubmed: 26947063
Bioinformatics. 2010 Jan 1;26(1):139-40
pubmed: 19910308
Development. 2017 Jan 15;144(2):175-186
pubmed: 28096211
Bioinformatics. 2009 May 1;25(9):1105-11
pubmed: 19289445
Nat Commun. 2017 Apr 21;8:15055
pubmed: 28429706
Sci Signal. 2014 Jan 21;7(309):ra9
pubmed: 24448649
Genome Biol. 2014 Feb 03;15(2):R29
pubmed: 24485249
Cell. 2008 Jun 13;133(6):1106-17
pubmed: 18555785
Proc Natl Acad Sci U S A. 2009 Nov 3;106(44):18722-7
pubmed: 19850877
Nat Cell Biol. 2018 May;20(5):610-619
pubmed: 29662178
Nature. 2016 Dec 1;540(7631):119-123
pubmed: 27880763
Mol Cell. 2013 Nov 21;52(4):495-505
pubmed: 24095279
Stem Cell Reports. 2015 Sep 8;5(3):314-22
pubmed: 26321140
Cell Stem Cell. 2016 Jan 7;18(1):118-33
pubmed: 26748758
Cell Stem Cell. 2014 Oct 2;15(4):416-430
pubmed: 25280218
EMBO J. 2012 May 2;31(9):2103-16
pubmed: 22446391
Cell Stem Cell. 2014 Oct 2;15(4):471-487
pubmed: 25090446
Cell. 2017 Apr 6;169(2):361-371
pubmed: 28388417
Oncogene. 2008 Sep 11;27(40):5339-47
pubmed: 18663353
Nature. 2015 Jun 11;522(7555):221-5
pubmed: 25896322
Science. 2014 Jan 3;343(6166):80-4
pubmed: 24336569
Nat Cell Biol. 2015 Dec;17(12):1523-35
pubmed: 26571212
Proc Natl Acad Sci U S A. 2017 Sep 19;114(38):10125-10130
pubmed: 28864533
Cell. 2008 Aug 8;134(3):521-33
pubmed: 18692474
Cell Cycle. 2011 Jul 15;10(14):2305-16
pubmed: 21670596
FEBS Lett. 2018 Mar;592(6):852-877
pubmed: 28834535
Proc Natl Acad Sci U S A. 2016 Oct 18;113(42):E6382-E6390
pubmed: 27698112
Trends Cell Biol. 2014 Jul;24(7):400-6
pubmed: 24698685

Auteurs

J Mathieu (J)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Comparative Medicine, University of Washington, Seattle, WA, 98109, USA.

D Detraux (D)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Laboratory of Cellular Biochemistry and Biology (URBC), University of Namur, Namur, 5000, Belgium.

D Kuppers (D)

Human Biology Division, Fred Hutchinson Cancer Research Center, Seattle, WA, 98109, USA.

Y Wang (Y)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Paul G. Allen School of Computer Science & Engineering, University of Washington, Seattle, WA, 98109, USA.

C Cavanaugh (C)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Comparative Medicine, University of Washington, Seattle, WA, 98109, USA.

S Sidhu (S)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

S Levy (S)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

A M Robitaille (AM)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Pharmacology, University of Washington, Seattle, WA, 98195, USA.

A Ferreccio (A)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

T Bottorff (T)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

A McAlister (A)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

L Somasundaram (L)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

F Artoni (F)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.

S Battle (S)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Medical Genetics & Genome Sciences, University of Washington, Seattle, WA, 98195, USA.

R D Hawkins (RD)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Medical Genetics & Genome Sciences, University of Washington, Seattle, WA, 98195, USA.

R T Moon (RT)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Pharmacology, University of Washington, Seattle, WA, 98195, USA.

C B Ware (CB)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA.
Department of Comparative Medicine, University of Washington, Seattle, WA, 98109, USA.

P J Paddison (PJ)

Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA. paddison@fredhutch.org.
Human Biology Division, Fred Hutchinson Cancer Research Center, Seattle, WA, 98109, USA. paddison@fredhutch.org.

H Ruohola-Baker (H)

Department of Biochemistry, University of Washington, Seattle, WA, 98195, USA. hannele@uw.edu.
Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, WA, 98109, USA. hannele@uw.edu.

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Classifications MeSH