Analysis of a Sardinian Multiplex Family with Autism Spectrum Disorder Points to Post-Synaptic Density Gene Variants and Identifies

ASD CAPG PSD proteins VDAC3 autism spectrum disorder postsynaptic density proteins

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
07 02 2019
Historique:
received: 15 01 2019
revised: 04 02 2019
accepted: 05 02 2019
entrez: 10 2 2019
pubmed: 10 2 2019
medline: 10 2 2019
Statut: epublish

Résumé

Autism spectrum disorders (ASDs) are a group of neurodevelopmental disorders with high heritability, although their underlying genetic factors are still largely unknown. Here we present a comprehensive genetic characterization of two ASD siblings from Sardinia by genome-wide copy number variation analysis and whole exome sequencing (WES), to identify novel genetic alterations associated with this disorder. Single nucleotide polymorphism (SNP) array data revealed a rare microdeletion involving

Identifiants

pubmed: 30736458
pii: jcm8020212
doi: 10.3390/jcm8020212
pmc: PMC6406497
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Fondazione Banco di Sardegna
ID : 1175/2009.0470
Pays : International
Organisme : Associazione Italiana Studio Malformazioni (ASM)
ID : 2010
Pays : International
Organisme : Fondo per la Ricerca Locale (ex 60%), Università di Cagliari
ID : 2010-2018
Pays : International
Organisme : Fondo per la Ricerca Fondamentale Orientata (ex quota 60%), Università di Bologna
ID : 2010-2018
Pays : International

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Auteurs

Elena Bacchelli (E)

Department of Pharmacy and Biotechnology, University of Bologna, 40126 Bologna, Italy. elena.bacchelli@unibo.it.

Eleonora Loi (E)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042 Cagliari, Italy. e.loi14@studenti.unica.it.

Cinzia Cameli (C)

Department of Pharmacy and Biotechnology, University of Bologna, 40126 Bologna, Italy. cinzia.cameli@gmail.com.

Loredana Moi (L)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042 Cagliari, Italy. lorymoi@gmail.com.

Ana Florencia Vega-Benedetti (AF)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042 Cagliari, Italy. aflvegabe@gmail.com.

Sylvain Blois (S)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042 Cagliari, Italy. slvbls@gmail.com.

Antonio Fadda (A)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042 Cagliari, Italy. fadda85@gmail.com.

Elena Bonora (E)

Department of Medical and Surgical Sciences, DIMEC, St. Orsola-Malpighi Hospital, University of Bologna, 40138 Bologna, Italy. elena.bonora6@unibo.it.

Sandra Mattu (S)

Department of Biomedical Sciences, Unit of Oncology and Molecular Pathology, University of Cagliari, 09124 Cagliari, Italy. mattu.sandra@yahoo.it.

Roberta Fadda (R)

Department of Pedagogy, Psychology, Philosophy, University of Cagliari, 09123 Cagliari, Italy. robfadda@gmail.com.

Rita Chessa (R)

Center for Pervasive Developmental Disorders, AO Brotzu, 09134 Cagliari, Italy. richess@libero.it.

Elena Maestrini (E)

Department of Pharmacy and Biotechnology, University of Bologna, 40126 Bologna, Italy. elena.maestrini@unibo.it.

Giuseppe Doneddu (G)

Center for Pervasive Developmental Disorders, AO Brotzu, 09134 Cagliari, Italy. iosettodoneddu@aob.it.

Patrizia Zavattari (P)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042 Cagliari, Italy. pzavattari@unica.it.

Classifications MeSH