[Survey on the Prevalence of Rare Kidney Diseases in Sicily].


Journal

Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologia
ISSN: 1724-5990
Titre abrégé: G Ital Nefrol
Pays: Italy
ID NLM: 9426434

Informations de publication

Date de publication:
Feb 2019
Historique:
entrez: 14 2 2019
pubmed: 14 2 2019
medline: 12 10 2019
Statut: ppublish

Résumé

Renal Diseases represent almost 6% of all Rare Diseases but are often misdiagnosed. In a survey made in Sicily in 2016, based on cases reported from all public hospitals according to a list of rare kidney diseases, we were able to collect 337 cases (199 males and 138 females). The highest prevalence was detected in children: 13.9 cases in 100.000 children; the mean age was 10, and the median 5 years, at the time of the diagnosis. Comparing our data with those available in the Sicilian Register of Rare Diseases we found that only 141 cases (54%) were present in the register. Promoting regional registries of rare kidney diseases in Italy may be useful for epidemiologic studies.

Identifiants

pubmed: 30758154
pii: 36-1-2019-9
pii:

Types de publication

Journal Article

Langues

ita

Sous-ensembles de citation

IM

Informations de copyright

Copyright by Società Italiana di Nefrologia SIN, Rome, Italy.

Auteurs

Silvio Maringhini (S)

Dipartimento Pediatria, Istituto Mediterraneo dei Trapianti e Tecniche specialistiche (ISMETT), Palermo, Italia.

Rosa Cusumano (R)

UOC Nefrologia Pediatrica, PO "G. Di Cristina", ARNAS Civico, Palermo, Italia.

Patrizia Miceli (P)

Dipartimento Attività Sanitarie Osservatorio Epidemiologico, Assessorato alla Salute, Regione Sicilia, Palermo, Italia.

Santina Castellino (S)

Università di Catania, Italia.

Roberto Chimenz (R)

UO Nefrologia e Reumatologia Pediatrica con Dialisi - AOU "G. Martino", Messina, Italia.

Gabriella Dardanoni (G)

Dipartimento Attività Sanitarie Osservatorio Epidemiologico, Assessorato alla Salute, Regione Sicilia, Palermo, Italia.

Angelo Ferrantelli (A)

UOC di Nefrologia e Dialisi, PO " V. Cervello", Palermo, Italia.

Antonio Granata (A)

UOC di Nefrologia e Dialisi, PO "San Giovanni di Dio", Agrigento, Italia.

Domenico Santoro (D)

UOC Nefrologia e Dialisi, Dip.to di Medicina Clinica e Sperimentale, Università degli studi di Messina, Italia.

Salvatore Scondotto (S)

Dipartimento Attività Sanitarie Osservatorio Epidemiologico, Assessorato alla Salute, Regione Sicilia, Palermo, Italia.

Articles similaires

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C
1.00
Humans Yoga Low Back Pain Female Male

Classifications MeSH