Adapting Proteostasis and Autophagy for Controlling the Pathogenesis of Cystic Fibrosis Lung Disease.
CFTR
ROS
autophagy
cystic fibrosis
protein-misfolding
proteostasis
Journal
Frontiers in pharmacology
ISSN: 1663-9812
Titre abrégé: Front Pharmacol
Pays: Switzerland
ID NLM: 101548923
Informations de publication
Date de publication:
2019
2019
Historique:
received:
27
09
2018
accepted:
09
01
2019
entrez:
19
2
2019
pubmed:
19
2
2019
medline:
19
2
2019
Statut:
epublish
Résumé
Cystic fibrosis (CF), a fatal genetic disorder predominant in the Caucasian population, is caused by mutations in the cystic fibrosis transmembrane conductance regulator (
Identifiants
pubmed: 30774592
doi: 10.3389/fphar.2019.00020
pmc: PMC6367269
doi:
Types de publication
Journal Article
Review
Langues
eng
Pagination
20Subventions
Organisme : NCRR NIH HHS
ID : UL1 RR025005
Pays : United States
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