Hedgehog signaling in the airway epithelium of patients with chronic obstructive pulmonary disease.


Journal

Scientific reports
ISSN: 2045-2322
Titre abrégé: Sci Rep
Pays: England
ID NLM: 101563288

Informations de publication

Date de publication:
04 03 2019
Historique:
received: 11 09 2018
accepted: 21 01 2019
entrez: 6 3 2019
pubmed: 6 3 2019
medline: 21 10 2020
Statut: epublish

Résumé

Genome-wide association studies have linked gene variants of the receptor patched homolog 1 (PTCH1) with chronic obstructive pulmonary disease (COPD). However, its biological role in the disease is unclear. Our objective was to determine the expression pattern and biological role of PTCH1 in the lungs of patients with COPD. Airway epithelial-specific PTCH1 protein expression and epithelial morphology were assessed in lung tissues of control and COPD patients. PTCH1 mRNA expression was measured in bronchial epithelial cells obtained from individuals with and without COPD. The effects of PTCH1 siRNA knockdown on epithelial repair and mucous expression were evaluated using human epithelial cell lines. Ptch1

Identifiants

pubmed: 30833624
doi: 10.1038/s41598-019-40045-3
pii: 10.1038/s41598-019-40045-3
pmc: PMC6399332
doi:

Substances chimiques

PTCH1 protein, human 0
Patched-1 Receptor 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

3353

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Auteurs

A Tam (A)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

M Hughes (M)

Biomedical Research Centre (BRC), University of British Columbia, Vancouver, British Columbia, Canada.

K M McNagny (KM)

Biomedical Research Centre (BRC), University of British Columbia, Vancouver, British Columbia, Canada.

M Obeidat (M)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

T L Hackett (TL)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.
Department of Anaesthesiology, Pharmacology, & Therapeutics, University of British Columbia, Vancouver, British Columbia, Canada.

J M Leung (JM)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

T Shaipanich (T)

Division of Respiratory Medicine, Department of Medicine, St. Paul's Hospital, University of British Columbia, Vancouver, British Columbia, Canada.

D R Dorscheid (DR)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

G K Singhera (GK)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

C W T Yang (CWT)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

P D Paré (PD)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

J C Hogg (JC)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada.

D Nickle (D)

Merck & Co. Inc., Rahway, New Jersey, United States of America.

D D Sin (DD)

Center for Heart Lung Innovation, St. Paul's Hospital, Vancouver, British Columbia, Canada. Don.Sin@hli.ubc.ca.

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