Integrated Analysis of Germline and Tumor DNA Identifies New Candidate Genes Involved in Familial Colorectal Cancer.

colorectal cancer computational genomics germline–tumor analysis mutational signatures predisposition to disease whole-exome sequencing

Journal

Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829

Informations de publication

Date de publication:
13 03 2019
Historique:
received: 25 01 2019
revised: 08 03 2019
accepted: 09 03 2019
entrez: 16 3 2019
pubmed: 16 3 2019
medline: 16 3 2019
Statut: epublish

Résumé

Colorectal cancer (CRC) shows aggregation in some families but no alterations in the known hereditary CRC genes. We aimed to identify new candidate genes which are potentially involved in germline predisposition to familial CRC. An integrated analysis of germline and tumor whole-exome sequencing data was performed in 18 unrelated CRC families. Deleterious single nucleotide variants (SNV), short insertions and deletions (indels), copy number variants (CNVs) and loss of heterozygosity (LOH) were assessed as candidates for first germline or second somatic hits. Candidate tumor suppressor genes were selected when alterations were detected in both germline and somatic DNA, fulfilling Knudson's two-hit hypothesis. Somatic mutational profiling and signature analysis were also performed. A series of germline-somatic variant pairs were detected. In all cases, the first hit was presented as a rare SNV/indel, whereas the second hit was either a different SNV (3 genes) or LOH affecting the same gene (141 genes).

Identifiants

pubmed: 30871259
pii: cancers11030362
doi: 10.3390/cancers11030362
pmc: PMC6468873
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Agència de Gestió d'Ajuts Universitaris i de Recerca
ID : 2018FI_B1_00213
Pays : International
Organisme : CIBEREHD
ID : CB06/04/0016
Pays : International
Organisme : Instituto de Salud Carlos III
ID : 17/00878
Pays : International
Organisme : Fundación Científica Asociación Española Contra el Cáncer
ID : GCB13131592CAST
Pays : International
Organisme : PERIS
ID : SLT002/16/00398
Pays : International
Organisme : Agència de Gestió d'Ajuts Universitaris i de Recerca
ID : GRPRE 2017SGR21
Pays : International
Organisme : Agència de Gestió d'Ajuts Universitaris i de Recerca
ID : GRC 2017SGR653
Pays : International
Organisme : European Cooperation in Science and Technology
ID : CA17118
Pays : International
Organisme : Generalitat de Catalunya
ID : CERCA programme
Pays : International

Références

PLoS Genet. 2016 Aug 09;12(8):e1006248
pubmed: 27504877
BMC Bioinformatics. 2018 Jun 14;19(1):224
pubmed: 29898651
Nat Rev Genet. 2016 Apr;17(4):224-38
pubmed: 26924765
Hum Mutat. 2014 Jul;35(7):899-907
pubmed: 24599517
PLoS One. 2015 Mar 17;10(3):e0120334
pubmed: 25781640
Hum Mol Genet. 2001 Dec 1;10(25):2869-77
pubmed: 11741830
F1000Res. 2016 Dec 5;5:2813
pubmed: 28105316
Ann Clin Biochem. 2015 Nov;52(Pt 6):690-2
pubmed: 26169059
Mol Cell. 2013 Mar 7;49(5):858-71
pubmed: 23333305
Bioinformatics. 2009 Jul 15;25(14):1754-60
pubmed: 19451168
Hum Mutat. 2018 Nov;39(11):1542-1552
pubmed: 30311369
Oncotarget. 2017 Jul 18;8(29):47064-47075
pubmed: 28423363
Nat Genet. 1998 Oct;20(2):184-8
pubmed: 9771713
BMC Genomics. 2012 Nov 24;13:666
pubmed: 23176052
Cancer Res. 2015 Jan 1;75(1):16-21
pubmed: 25381154
Fam Cancer. 2016 Apr;15(2):281-8
pubmed: 26780541
Genome Res. 2010 Sep;20(9):1297-303
pubmed: 20644199
Breast Cancer Res Treat. 2009 Feb;113(3):545-51
pubmed: 18302019
Cell Rep. 2013 Jan 31;3(1):246-59
pubmed: 23318258
Mol Cell. 2013 Mar 7;49(5):872-83
pubmed: 23333306
Nat Genet. 2009 Aug;41(8):936-40
pubmed: 19561605
Nat Rev Genet. 2015 Mar;16(3):172-83
pubmed: 25645873
PLoS Genet. 2008 Jul;4(7):e1000115
pubmed: 18852846
Nat Genet. 2015 Jun;47(6):643-6
pubmed: 25915596
Nat Genet. 1997 May;16(1):64-7
pubmed: 9140396
Am J Epidemiol. 2017 Feb 1;185(3):224-237
pubmed: 28073766
J Biol Chem. 2001 Nov 9;276(45):42259-67
pubmed: 11533059
N Engl J Med. 2000 Jul 13;343(2):78-85
pubmed: 10891514
J Genet Genomics. 2018 Jan 20;45(1):41-45
pubmed: 29396139
Cancer Res. 2014 Dec 1;74(23):6947-57
pubmed: 25320007
Genet Med. 2015 Feb;17(2):131-42
pubmed: 25058500
Proc Natl Acad Sci U S A. 1971 Apr;68(4):820-3
pubmed: 5279523
Nat Genet. 2016 Jun;48(6):600-606
pubmed: 27111033
Int J Cancer. 2019 Apr 15;144(8):1941-1953
pubmed: 30350310
Oncotarget. 2013 Oct;4(10):1791-803
pubmed: 24113161
Nature. 2014 Jan 16;505(7483):302-8
pubmed: 24429628
Nat Commun. 2018 Jul 4;9(1):2601
pubmed: 29973584
Nucleic Acids Res. 2017 Jan 4;45(D1):D777-D783
pubmed: 27899578
Hum Mol Genet. 1994 Oct;3(10):1783-8
pubmed: 7849702
Cell. 2017 Nov 16;171(5):1042-1056.e10
pubmed: 29056344
Nature. 2013 Aug 22;500(7463):415-21
pubmed: 23945592
Eur J Hum Genet. 2016 Oct;24(10):1501-5
pubmed: 27165003
CA Cancer J Clin. 2018 Nov;68(6):394-424
pubmed: 30207593
Clin Gastroenterol Hepatol. 2017 Jun;15(6):809-819
pubmed: 27712984
Am J Hum Genet. 2015 Nov 5;97(5):661-76
pubmed: 26522472
Stat Appl Genet Mol Biol. 2009;8:Article 47
pubmed: 19954419
Gastroenterology. 2010 Jun;138(6):2044-58
pubmed: 20420945
Brief Bioinform. 2013 Mar;14(2):178-92
pubmed: 22517427
J Clin Invest. 1998 Oct 15;102(8):1599-608
pubmed: 9788974
Biochem J. 2006 Sep 15;398(3):319-37
pubmed: 16925525
Am J Hum Genet. 2018 Jul 5;103(1):19-29
pubmed: 29887214

Auteurs

Marcos Díaz-Gay (M)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. diaz2@clinic.cat.

Sebastià Franch-Expósito (S)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. sebasfranch@gmail.com.

Coral Arnau-Collell (C)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. arnau@clinic.cat.

Solip Park (S)

Systems Biology Program, Centre for Genomic Regulation (CRG), The Barcelona Institute of Science and Technology, 08003 Barcelona, Spain. imagineyd@gmail.com.

Fran Supek (F)

Institut de Recerca Biomedica (IRB Barcelona), The Barcelona Institute of Science and Technology, 08028 Barcelona, Spain. fran.supek@irbbarcelona.org.

Jenifer Muñoz (J)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. jenifer.munoz@ciberehd.org.

Laia Bonjoch (L)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. bonjoch@clinic.cat.

Anna Gratacós-Mulleras (A)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. annagratacosm@gmail.com.

Paula A Sánchez-Rojas (PA)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. paulasanchez10@live.com.

Clara Esteban-Jurado (C)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. darth.clara@gmail.com.

Teresa Ocaña (T)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. mocana@clinic.cat.

Miriam Cuatrecasas (M)

Pathology Department, Hospital Clínic, 08036 Barcelona, Spain. mcuatrec@clinic.cat.

Maria Vila-Casadesús (M)

Bioinformatics Platform, Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), 08036 Barcelona, Spain. maria.vila.cs@gmail.com.

Juan José Lozano (JJ)

Bioinformatics Platform, Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), 08036 Barcelona, Spain. juanjo.lozano@ciberehd.org.

Genis Parra (G)

Centre Nacional d'Anàlisi Genòmica-Centre de Regulació Genòmica (CNAG-CRG), Parc Científic de Barcelona, 08028 Barcelona, Spain. genis.parra@cnag.crg.eu.

Steve Laurie (S)

Centre Nacional d'Anàlisi Genòmica-Centre de Regulació Genòmica (CNAG-CRG), Parc Científic de Barcelona, 08028 Barcelona, Spain. steven.laurie@cnag.crg.eu.

Sergi Beltran (S)

Centre Nacional d'Anàlisi Genòmica-Centre de Regulació Genòmica (CNAG-CRG), Parc Científic de Barcelona, 08028 Barcelona, Spain. sergi.beltran@cnag.crg.eu.
Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. luis.bujandafernandezdepierola@osakidetza.eus.
Gastroenterology Department, Hospital Donostia-Instituto Biodonostia, Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Basque Country University (UPV/EHU), 20014 San Sebastián, Spain. luis.bujandafernandezdepierola@osakidetza.eus.
Gastroenterology Department, Complexo Hospitalario Universitario de Ourense, Instituto de Investigación Sanitaria Galicia Sur, 32005 Ourense, Spain. luis.bujandafernandezdepierola@osakidetza.eus.

Antoni Castells (A)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. castells@clinic.cat.

Luis Bujanda (L)

Gastroenterology Department, Hospital Donostia-Instituto Biodonostia, Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Basque Country University (UPV/EHU), 20014 San Sebastián, Spain. luis.bujandafernandezdepierola@osakidetza.eus.

Joaquín Cubiella (J)

Gastroenterology Department, Complexo Hospitalario Universitario de Ourense, Instituto de Investigación Sanitaria Galicia Sur, 32005 Ourense, Spain. joaquin.cubiella.fernandez@sergas.es.

Francesc Balaguer (F)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. fprunes@clinic.cat.

Sergi Castellví-Bel (S)

Gastroenterology Department, Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas (CIBERehd), Hospital Clínic, 08036 Barcelona, Spain. sbel@clinic.cat.

Classifications MeSH