An Assay to Determine Mechanisms of Rapid Autoantibody-Induced Neurotransmitter Receptor Endocytosis and Vesicular Trafficking in Autoimmune Encephalitis.

N-Methyl-D-aspartate receptors autoantibodies autoimmune encephalitis cross-linking endocytosis exocytosis vesicular trafficking

Journal

Frontiers in neurology
ISSN: 1664-2295
Titre abrégé: Front Neurol
Pays: Switzerland
ID NLM: 101546899

Informations de publication

Date de publication:
2019
Historique:
received: 19 09 2018
accepted: 11 02 2019
entrez: 19 3 2019
pubmed: 19 3 2019
medline: 19 3 2019
Statut: epublish

Résumé

N-Methyl-D-aspartate (NMDA) receptors (NMDARs) are among the most important excitatory neurotransmitter receptors in the human brain. Autoantibodies to the human NMDAR cause the most frequent form of autoimmune encephalitis involving autoantibody-mediated receptor cross-linking and subsequent internalization of the antibody-receptor complex. This has been deemed to represent the predominant antibody effector mechanism depleting the NMDAR from the synaptic and extra-synaptic neuronal cell membrane. To assess in detail the molecular mechanisms of autoantibody-induced NMDAR endocytosis, vesicular trafficking, and exocytosis we transiently co-expressed rat GluN1-1a-EGFP and GluN2B-ECFP alone or together with scaffolding postsynaptic density protein 95 (PSD-95), wild-type (WT), or dominant-negative (DN) mutant Ras-related in brain (RAB) proteins (RAB5WT, RAB5DN, RAB11WT, RAB11DN) in HEK 293T cells. The cells were incubated with a pH-rhodamine-labeled human recombinant monoclonal GluN1 IgG1 autoantibody (GluN1-aAb

Identifiants

pubmed: 30881339
doi: 10.3389/fneur.2019.00178
pmc: PMC6405626
doi:

Types de publication

Journal Article

Langues

eng

Pagination

178

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Auteurs

Elsie Amedonu (E)

Myocellular Electrophysiology and Molecular Biology, Institute for Genetics of Heart Diseases, University of Muenster, Muenster, Germany.
Department of Neurology, University of Muenster, Muenster, Germany.

Christoph Brenker (C)

Centre of Reproductive Medicine and Andrology, University of Muenster, Muenster, Germany.

Sumanta Barman (S)

Department of Neurology, Universitätsklinikum and Center for Neurology and Neuropsychiatry LVR Klinikum, Heinrich Heine University Duesseldorf, Duesseldorf, Germany.

Julian A Schreiber (JA)

Myocellular Electrophysiology and Molecular Biology, Institute for Genetics of Heart Diseases, University of Muenster, Muenster, Germany.

Sebastian Becker (S)

Myocellular Electrophysiology and Molecular Biology, Institute for Genetics of Heart Diseases, University of Muenster, Muenster, Germany.

Stefan Peischard (S)

Myocellular Electrophysiology and Molecular Biology, Institute for Genetics of Heart Diseases, University of Muenster, Muenster, Germany.

Nathalie Strutz-Seebohm (N)

Myocellular Electrophysiology and Molecular Biology, Institute for Genetics of Heart Diseases, University of Muenster, Muenster, Germany.

Christine Strippel (C)

Department of Neurology, University of Muenster, Muenster, Germany.

Andre Dik (A)

Department of Neurology, University of Muenster, Muenster, Germany.

Hans-Peter Hartung (HP)

Department of Neurology, Universitätsklinikum and Center for Neurology and Neuropsychiatry LVR Klinikum, Heinrich Heine University Duesseldorf, Duesseldorf, Germany.

Thomas Budde (T)

Institute for Physiology I, University of Muenster, Muenster, Germany.

Heinz Wiendl (H)

Department of Neurology, University of Muenster, Muenster, Germany.

Timo Strünker (T)

Centre of Reproductive Medicine and Andrology, University of Muenster, Muenster, Germany.

Bernhard Wünsch (B)

Institute for Pharmaceutical and Medical Chemistry, University of Muenster, Muenster, Germany.

Norbert Goebels (N)

Department of Neurology, Universitätsklinikum and Center for Neurology and Neuropsychiatry LVR Klinikum, Heinrich Heine University Duesseldorf, Duesseldorf, Germany.

Sven G Meuth (SG)

Department of Neurology, University of Muenster, Muenster, Germany.

Guiscard Seebohm (G)

Myocellular Electrophysiology and Molecular Biology, Institute for Genetics of Heart Diseases, University of Muenster, Muenster, Germany.

Nico Melzer (N)

Department of Neurology, University of Muenster, Muenster, Germany.

Classifications MeSH