Interaction between galectin-3 and cystinosin uncovers a pathogenic role of inflammation in kidney involvement of cystinosis.


Journal

Kidney international
ISSN: 1523-1755
Titre abrégé: Kidney Int
Pays: United States
ID NLM: 0323470

Informations de publication

Date de publication:
08 2019
Historique:
received: 18 07 2018
revised: 11 12 2018
accepted: 10 01 2019
pubmed: 1 4 2019
medline: 2 10 2020
entrez: 1 4 2019
Statut: ppublish

Résumé

Inflammation is involved in the pathogenesis of many disorders. However, the underlying mechanisms are often unknown. Here, we test whether cystinosin, the protein involved in cystinosis, is a critical regulator of galectin-3, a member of the β-galactosidase binding protein family, during inflammation. Cystinosis is a lysosomal storage disorder and, despite ubiquitous expression of cystinosin, the kidney is the primary organ impacted by the disease. Cystinosin was found to enhance lysosomal localization and degradation of galectin-3. In Ctns

Identifiants

pubmed: 30928021
pii: S0085-2538(19)30172-3
doi: 10.1016/j.kint.2019.01.029
pmc: PMC7269416
mid: NIHMS1585184
pii:
doi:

Substances chimiques

Amino Acid Transport Systems, Neutral 0
Ccl2 protein, mouse 0
Chemokine CCL2 0
Galectin 3 0
Lgals3 protein, mouse 0
cystinosin protein, mouse 0
Cystine 48TCX9A1VT

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't Research Support, U.S. Gov't, Non-P.H.S.

Langues

eng

Sous-ensembles de citation

IM

Pagination

350-362

Subventions

Organisme : NHLBI NIH HHS
ID : R01 HL088256
Pays : United States
Organisme : NIDDK NIH HHS
ID : R01 DK110162
Pays : United States
Organisme : NINDS NIH HHS
ID : P30 NS047101
Pays : United States
Organisme : NIDDK NIH HHS
ID : R01 DK090058
Pays : United States
Organisme : NEI NIH HHS
ID : R21 EY028642
Pays : United States

Commentaires et corrections

Type : CommentIn

Informations de copyright

Copyright © 2019 International Society of Nephrology. Published by Elsevier Inc. All rights reserved.

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Auteurs

Tatiana Lobry (T)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA; INSERM, U1078, Équipe 'Transfert de gènes et thérapie génique', Faculté de Médecine, Brest, France, and CHRU de Brest, Service de Génétique Moléculaire et d'histocompatibilité, Brest, France.

Roy Miller (R)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA.

Nathalie Nevo (N)

INSERM, U1163, Imagine Institute, Laboratory of Hereditary Kidney Diseases, Paris, France; Paris Descartes-Sorbonne Paris Cité University, Paris, France.

Celine J Rocca (CJ)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA.

Jinzhong Zhang (J)

Department of Molecular Medicine, The Scripps Research Institute, La Jolla, California, USA.

Sergio D Catz (SD)

Department of Molecular Medicine, The Scripps Research Institute, La Jolla, California, USA.

Fiona Moore (F)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA.

Lucie Thomas (L)

INSERM, U1163, Imagine Institute, Laboratory of Hereditary Kidney Diseases, Paris, France; Paris Descartes-Sorbonne Paris Cité University, Paris, France.

Daniel Pouly (D)

INSERM, U1163, Imagine Institute, Laboratory of Hereditary Kidney Diseases, Paris, France; Paris Descartes-Sorbonne Paris Cité University, Paris, France.

Anne Bailleux (A)

INSERM, U1163, Imagine Institute, Laboratory of Hereditary Kidney Diseases, Paris, France; Paris Descartes-Sorbonne Paris Cité University, Paris, France.

Ida Chiara Guerrera (IC)

Proteomics Platform 3P5-Necker, Université Paris Descartes-Structure Fédérative de Recherche Necker, INSERM US24/CNRS UMS3633, Paris, France.

Marie-Claire Gubler (MC)

INSERM, U1163, Imagine Institute, Laboratory of Hereditary Kidney Diseases, Paris, France; Paris Descartes-Sorbonne Paris Cité University, Paris, France.

Wai W Cheung (WW)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA.

Robert H Mak (RH)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA.

Tristan Montier (T)

INSERM, U1078, Équipe 'Transfert de gènes et thérapie génique', Faculté de Médecine, Brest, France, and CHRU de Brest, Service de Génétique Moléculaire et d'histocompatibilité, Brest, France.

Corinne Antignac (C)

INSERM, U1163, Imagine Institute, Laboratory of Hereditary Kidney Diseases, Paris, France; Paris Descartes-Sorbonne Paris Cité University, Paris, France; Department of Genetics, Necker Hospital, Assistance Publique-Hôpitaux de Paris, Paris, France.

Stephanie Cherqui (S)

Department of Pediatrics, Division of Genetics, University of California, San Diego, La Jolla, California, USA. Electronic address: scherqui@ucsd.edu.

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Classifications MeSH