Recessive Mutations in


Journal

Hepatology communications
ISSN: 2471-254X
Titre abrégé: Hepatol Commun
Pays: United States
ID NLM: 101695860

Informations de publication

Date de publication:
Apr 2019
Historique:
received: 24 10 2018
accepted: 11 01 2019
entrez: 13 4 2019
pubmed: 13 4 2019
medline: 13 4 2019
Statut: epublish

Résumé

Undiagnosed liver disease remains an unmet medical need in pediatric hepatology, including children with high gamma-glutamyltransferase (GGT) cholestasis. Here, we report whole-exome sequencing of germline DNA from 2 unrelated children, both offspring of consanguineous union, with neonatal cholestasis and high GGT of unclear etiology. Both children had a rare homozygous damaging mutation (p.Arg219* and p.Val204Met) in kinesin family member 12 (

Identifiants

pubmed: 30976738
doi: 10.1002/hep4.1320
pii: HEP41320
pmc: PMC6442693
doi:

Types de publication

Journal Article

Langues

eng

Pagination

471-477

Subventions

Organisme : NIDDK NIH HHS
ID : P30 DK034989
Pays : United States
Organisme : NIH HHS
ID : S10 OD018521
Pays : United States
Organisme : NCATS NIH HHS
ID : UL1 TR001863
Pays : United States

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Auteurs

Aysel Ünlüsoy Aksu (A)

Department of Pediatric Gastroenterology, Hepatology and Nutrition University of Health Sciences, Dr. Sami Ulus Maternity and Child Health and Diseases Training and Research Hospital Ankara Turkey.

Subhash K Das (SK)

Department of Internal Medicine, Section of Digestive Diseases Yale University School of Medicine New Haven CT.

Carol Nelson-Williams (C)

Department of Genetics Yale University School of Medicine New Haven CT.

Dhanpat Jain (D)

Department of Internal Medicine, Section of Digestive Diseases Yale University School of Medicine New Haven CT.
Department of Pathology Yale University School of Medicine New Haven CT.

Ferda Özbay Hoşnut (F)

Department of Pediatric Gastroenterology, Hepatology and Nutrition University of Health Sciences, Dr. Sami Ulus Maternity and Child Health and Diseases Training and Research Hospital Ankara Turkey.

Gülseren Evirgen Şahin (G)

Department of Pediatric Gastroenterology, Hepatology and Nutrition University of Health Sciences, Dr. Sami Ulus Maternity and Child Health and Diseases Training and Research Hospital Ankara Turkey.

Richard P Lifton (RP)

Department of Genetics Yale University School of Medicine New Haven CT.
Yale Center for Mendelian Genomics Yale University School of Medicine New Haven CT.
Laboratory of Human Genetics and Genomics Rockefeller University New York NY.

Silvia Vilarinho (S)

Department of Internal Medicine, Section of Digestive Diseases Yale University School of Medicine New Haven CT.
Department of Pathology Yale University School of Medicine New Haven CT.

Classifications MeSH