PANDAS/PANS in childhood: Controversies and evidence.

Autoimmune OCD Paediatric Psychiatric Tics

Journal

Paediatrics & child health
ISSN: 1205-7088
Titre abrégé: Paediatr Child Health
Pays: England
ID NLM: 9815960

Informations de publication

Date de publication:
May 2019
Historique:
received: 23 04 2018
accepted: 13 07 2018
entrez: 19 4 2019
pubmed: 19 4 2019
medline: 19 4 2019
Statut: ppublish

Résumé

Since first defined in 1998, paediatric autoimmune neuropsychiatric disorders associated with streptococcal infections (PANDAS) and its later, broader iteration, paediatric acute-onset neuropsychiatric syndrome (PANS), have garnered significant attention and controversy. The role of streptococcal infection in children with explosive onset obsessive-compulsive disorder and new onset tics, the natural history of this entity, and the role of symptomatic and disease-modifying therapies, including antibiotics, immunotherapy, and psychoactive drugs, are all issues that have yet to be definitively addressed. While definitive proof of the autoimmune hypothesis of PANDAS is lacking, given the heightened attention to this entity and apparent rise in use of this diagnostic category, addressing questions around diagnosis, treatment, and etiology is imperative. In this paper, we review current working definitions of PANDAS/PANS, discuss published evidence for interventions related to this entity, and propose a clinical approach to children presenting with acute symptoms satisfying criteria for PANDAS/PANS.

Identifiants

pubmed: 30996598
doi: 10.1093/pch/pxy145
pii: pxy145
pmc: PMC6462125
doi:

Types de publication

Journal Article

Langues

eng

Pagination

85-91

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Auteurs

Colin Wilbur (C)

Division of Neurology, The Hospital for Sick Children, Toronto, Ontario, Canada.
Division of Neuroscience and Mental Health, The Hospital for Sick Children Research Institute, Toronto, Ontario, Canada.

Ari Bitnun (A)

Division of Infectious Diseases, The Hospital for Sick Children, Toronto, Ontario, Canada.
Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.

Sefi Kronenberg (S)

Department of Psychiatry, The Hospital for Sick Children, Toronto, Ontario, Canada.
Department of Psychiatry, University of Toronto, Toronto, Ontario, Canada.

Ronald M Laxer (RM)

Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.
Division of Rheumatology, The Hospital for Sick Children, Toronto, Ontario, Canada.

Deborah M Levy (DM)

Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.
Division of Rheumatology, The Hospital for Sick Children, Toronto, Ontario, Canada.

William J Logan (WJ)

Division of Neurology, The Hospital for Sick Children, Toronto, Ontario, Canada.
Division of Neuroscience and Mental Health, The Hospital for Sick Children Research Institute, Toronto, Ontario, Canada.
Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.

Michelle Shouldice (M)

Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.
Division of Pediatric Medicine, The Hospital for Sick Children, Toronto, Ontario, Canada.

E Ann Yeh (EA)

Division of Neurology, The Hospital for Sick Children, Toronto, Ontario, Canada.
Division of Neuroscience and Mental Health, The Hospital for Sick Children Research Institute, Toronto, Ontario, Canada.
Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.

Classifications MeSH