Lactulose to the Rescue: A Case of Toxic Hepatic Encephalopathy Caused by Portosystemic Shunting and Epistaxis in a Patient with Hereditary Hemorrhagic Telangiectasia.


Journal

Case reports in hepatology
ISSN: 2090-6587
Titre abrégé: Case Reports Hepatol
Pays: United States
ID NLM: 101622103

Informations de publication

Date de publication:
2019
Historique:
received: 16 01 2019
accepted: 14 03 2019
entrez: 30 4 2019
pubmed: 30 4 2019
medline: 30 4 2019
Statut: epublish

Résumé

Hereditary hemorrhagic telangiectasia (HHT) is an uncommon autosomal dominant disorder characterized by telangiectasias and arteriovenous malformations. Multiple organ systems are involved including the skin, lungs, gastrointestinal tract, and brain. Hepatic encephalopathy is an extremely rare complication of HHT and early diagnosis and treatment can be life-saving. We present a rare case of hepatic encephalopathy caused by HHT-induced portosystemic shunting treated with lactulose.

Identifiants

pubmed: 31032126
doi: 10.1155/2019/7573408
pmc: PMC6457288
doi:

Types de publication

Case Reports

Langues

eng

Pagination

7573408

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Auteurs

Ruchit N Shah (RN)

Geisinger Medical Center, Department of Internal Medicine, 100 N Academy Ave, Danville, PA 17822, USA.
Geisinger Commonwealth School of Medicine, 525 Pine Street, Scranton, PA 18510, USA.

Michael Makar (M)

Geisinger Commonwealth School of Medicine, 525 Pine Street, Scranton, PA 18510, USA.

Nasir Akhtar (N)

Geisinger Medical Center, Department of Gastroenterology, 100 N Academy Ave, Danville, PA 17822, USA.

Erin Forster (E)

Geisinger Medical Center, Department of Gastroenterology, 100 N Academy Ave, Danville, PA 17822, USA.
Medical University of South Carolina, 30 Courtenay Dr, Charleston, SC 29425, USA.

Classifications MeSH