Unguarded left atrioventricular orifice: An unusual cause of hypoplastic left ventricle and double-outlet right ventricle with intact ventricular septum.
Congenital mitral valve absence
double-outlet right ventricle
hypoplastic left ventricle
Journal
Annals of pediatric cardiology
ISSN: 0974-2069
Titre abrégé: Ann Pediatr Cardiol
Pays: India
ID NLM: 101495459
Informations de publication
Date de publication:
Historique:
entrez:
31
5
2019
pubmed:
31
5
2019
medline:
31
5
2019
Statut:
ppublish
Résumé
An unguarded atrioventricular orifice is an extremely rare congenital anomaly characterized by the absence of the atrioventricular valve in varying proportions. While atresia of the mitral or aortic valves are usually described as causes for hypoplastic left heart, our case highlights the role of free atrioventricular valve regurgitation and consequent volume loss of the left heart, giving rise to a small left ventricle. There was an associated double-outlet right ventricle and Type B aortic interruption. While we have attempted to discuss the complex management options in this scenario, the parents decided to withdraw further care.
Identifiants
pubmed: 31143045
doi: 10.4103/apc.APC_124_18
pii: APC-12-153
pmc: PMC6521664
doi:
Types de publication
Case Reports
Langues
eng
Pagination
153-155Déclaration de conflit d'intérêts
There are no conflicts of interest.
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