In vitro bone-like nodules generated from patient-derived iPSCs recapitulate pathological bone phenotypes.
Animals
Bone Morphogenetic Proteins
Bone and Bones
/ drug effects
Cell Differentiation
Cells, Cultured
Gene Expression Regulation
Humans
In Vitro Techniques
Induced Pluripotent Stem Cells
/ drug effects
Male
Mice
Mice, Nude
Mice, SCID
Mutation
Osteogenesis
/ drug effects
Phenotype
Receptors, Retinoic Acid
/ drug effects
TOR Serine-Threonine Kinases
/ drug effects
Transplantation
Tretinoin
/ pharmacology
Wnt Signaling Pathway
Journal
Nature biomedical engineering
ISSN: 2157-846X
Titre abrégé: Nat Biomed Eng
Pays: England
ID NLM: 101696896
Informations de publication
Date de publication:
07 2019
07 2019
Historique:
received:
22
01
2018
accepted:
30
04
2019
pubmed:
12
6
2019
medline:
10
3
2020
entrez:
12
6
2019
Statut:
ppublish
Résumé
The recapitulation of bone formation via the in vitro generation of bone-like nodules is frequently used to understand bone development. However, current bone-induction techniques are slow and difficult to reproduce. Here, we report the formation of bone-like nodules within ten days, via the use of retinoic acid (RA) to induce the osteogenic differentiation of human induced pluripotent stem cells (hiPSCs) into osteoblast-like and osteocyte-like cells that create human bone tissue when implanted in calvarial defects in mice. We also show that the induction of bone formation depends on cell signalling through the RA receptors RARα and RARβ, which simultaneously activate the BMP (bone morphogenetic protein) and Wnt signalling pathways. Moreover, by using patient-derived hiPSCs, the bone-like nodules recapitulated the osteogenesis-imperfecta phenotype, which was rescued via the correction of disease-causing mutations and partially by an mTOR (mechanistic target of rapamycin) inhibitor. The method of inducing bone nodules may serve as a fast and reproducible model for the study of the formation of both healthy and pathological bone.
Identifiants
pubmed: 31182836
doi: 10.1038/s41551-019-0410-7
pii: 10.1038/s41551-019-0410-7
doi:
Substances chimiques
Bone Morphogenetic Proteins
0
Receptors, Retinoic Acid
0
Tretinoin
5688UTC01R
TOR Serine-Threonine Kinases
EC 2.7.11.1
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM