Variant form of hairy cell leukemia.

BRAFV600E Ibrutinib KDM6A chronic B‐lymphoproliferative disorder hairy cell leukemia hairy cell leukemia variant

Journal

Clinical case reports
ISSN: 2050-0904
Titre abrégé: Clin Case Rep
Pays: England
ID NLM: 101620385

Informations de publication

Date de publication:
Jun 2019
Historique:
received: 05 11 2018
revised: 17 03 2019
accepted: 08 04 2019
entrez: 12 6 2019
pubmed: 12 6 2019
medline: 12 6 2019
Statut: epublish

Résumé

Mature lymphoid B-cell proliferations with hairy cells represent heterogeneous entities where specific diagnosis is difficult but important since it impacts therapeutic management. The clinical cases of variant hairy cell leukemia reported herein illustrate the persistence of a clear interest in the use of splenectomy as a therapeutic alternative. Furthermore, ibrutinib appears to be a promising treatment in patients with relapsed/refractory disease.

Identifiants

pubmed: 31183086
doi: 10.1002/ccr3.2176
pii: CCR32176
pmc: PMC6552962
doi:

Types de publication

Case Reports

Langues

eng

Pagination

1161-1166

Déclaration de conflit d'intérêts

None declared.

Références

Ann Pathol. 2010 Jun;30(3):206-10
pubmed: 20621598
Clin Case Rep. 2019 May 06;7(6):1161-1166
pubmed: 31183086
Leukemia. 2018 Aug;32(8):1768-1777
pubmed: 30030507
Hematol Oncol Clin North Am. 2006 Oct;20(5):1051-63
pubmed: 16990106
Best Pract Res Clin Haematol. 2015 Dec;28(4):253-63
pubmed: 26614904
Int Rev Immunol. 2012 Apr;31(2):119-32
pubmed: 22449073
Ann Oncol. 2015 Sep;26 Suppl 5:v100-7
pubmed: 26269205
Br J Haematol. 2014 Jul;166(2):177-88
pubmed: 24697238
Blood. 2016 May 19;127(20):2375-90
pubmed: 26980727
Ann Biol Clin (Paris). 2015 Jul-Aug;73(4):399-406
pubmed: 25858127
Nat Rev Cancer. 2014 Apr;14(4):219-32
pubmed: 24658273
Blood. 2017 Feb 23;129(8):1042-1045
pubmed: 28069605
F1000Res. 2018 Mar 28;7:406
pubmed: 29657712
Haematologica. 2017 Oct;102(10):1758-1766
pubmed: 28751561
Oncotarget. 2018 Jun 22;9(48):28866-28876
pubmed: 29989027
Blood Res. 2018 Mar;53(1):74-78
pubmed: 29662866
Nat Genet. 2014 Jan;46(1):8-10
pubmed: 24241536
Am J Hematol. 2017 Dec;92(12):1382-1390
pubmed: 29110361
Discov Med. 2012 Apr;13(71):253-65
pubmed: 22541613
N Engl J Med. 2011 Jun 16;364(24):2305-15
pubmed: 21663470
Haematologica. 2010 Jul;95(7):1122-9
pubmed: 20220064
Leuk Res. 2016 May;44:53-60
pubmed: 27030961

Auteurs

Margaux Wiber (M)

Laboratoire d'Hématologie CHU Caen Caen France.

Elsa Maitre (E)

Laboratoire d'Hématologie CHU Caen Caen France.
Normandie Université, INSERM U1245 Université de Caen Caen France.

Edouard Cornet (E)

Laboratoire d'Hématologie CHU Caen Caen France.
Normandie Université, INSERM U1245 Université de Caen Caen France.

Véronique Salaün (V)

Laboratoire d'Hématologie CHU Caen Caen France.

Dina Naguib (D)

Laboratoire d'Hématologie CHU Caen Caen France.

Xavier Troussard (X)

Laboratoire d'Hématologie CHU Caen Caen France.
Normandie Université, INSERM U1245 Université de Caen Caen France.
Institut d'Hématologie de Basse-Normandie CHU Caen Caen France.

Classifications MeSH