Novel Mutations and Unreported Clinical Features in KBG Syndrome.

16q24.3 deletion ANKRD11 Joint stiffness KBG syndrome Macrodontia

Journal

Molecular syndromology
ISSN: 1661-8769
Titre abrégé: Mol Syndromol
Pays: Switzerland
ID NLM: 101525192

Informations de publication

Date de publication:
May 2019
Historique:
accepted: 03 12 2018
entrez: 14 6 2019
pubmed: 14 6 2019
medline: 14 6 2019
Statut: ppublish

Résumé

KBG syndrome is an autosomal dominant disorder caused by pathogenic variants within

Identifiants

pubmed: 31191201
doi: 10.1159/000496172
pii: msy-0010-0130
pmc: PMC6528090
doi:

Types de publication

Case Reports

Langues

eng

Pagination

130-138

Références

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Auteurs

Emanuela Scarano (E)

Rare Disease Unit, Department of Pediatrics, St. Orsola-Malpighi Hospital, Bologna, Italy.

Martina Tassone (M)

Rare Disease Unit, Department of Pediatrics, St. Orsola-Malpighi Hospital, Bologna, Italy.

Claudio Graziano (C)

Unit of Medical Genetics, Department of Medical and Surgical Sciences, University Alma Mater Studiorum, St. Orsola-Malpighi Hospital, Bologna, Italy.

Dino Gibertoni (D)

Unit of Hygiene and Medical Statistics, Department of Biomedical and Neuromotor Sciences, University Alma Mater Studiorum, Bologna, Italy.

Federica Tamburrino (F)

Rare Disease Unit, Department of Pediatrics, St. Orsola-Malpighi Hospital, Bologna, Italy.

Annamaria Perri (A)

Rare Disease Unit, Department of Pediatrics, St. Orsola-Malpighi Hospital, Bologna, Italy.

Maria Gnazzo (M)

Laboratory of Medical Genetics, Bambino Gesù Pediatric Hospital, IRCCS, Rome, Italy.

Giulia Severi (G)

Unit of Medical Genetics, Department of Medical and Surgical Sciences, University Alma Mater Studiorum, St. Orsola-Malpighi Hospital, Bologna, Italy.

Francesca Lepri (F)

Laboratory of Medical Genetics, Bambino Gesù Pediatric Hospital, IRCCS, Rome, Italy.

Laura Mazzanti (L)

Rare Disease Unit, Department of Pediatrics, St. Orsola-Malpighi Hospital, Bologna, Italy.

Classifications MeSH