Blepharophimosis, Ptosis, Epicanthus Inversus Syndrome: New Report with a 197-kb Deletion Upstream of

3q23 deletion Anti-müllerian hormone BPES COPB2 FOXL2 Inhibin B MRPS22 Ovarian function Regulatory elements array CGH

Journal

Molecular syndromology
ISSN: 1661-8769
Titre abrégé: Mol Syndromol
Pays: Switzerland
ID NLM: 101525192

Informations de publication

Date de publication:
May 2019
Historique:
accepted: 17 12 2018
entrez: 14 6 2019
pubmed: 14 6 2019
medline: 14 6 2019
Statut: ppublish

Résumé

Blepharophimosis, ptosis, and epicanthus inversus syndrome (BPES) is due to heterozygous

Identifiants

pubmed: 31191203
doi: 10.1159/000497092
pii: msy-0010-0147
pmc: PMC6528085
doi:

Types de publication

Journal Article

Langues

eng

Pagination

147-153

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Auteurs

Veronica Bertini (V)

SOD Citogenetica, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Angelo Valetto (A)

SOD Citogenetica, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Fulvia Baldinotti (F)

SOD Genetica Molecolare, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Alessia Azzarà (A)

SOD Citogenetica, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Francesca Cambi (F)

SOD Citogenetica, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Benedetta Toschi (B)

Sezione Genetica Medica, Medicina Interna 1, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Alessandro Giacomina (A)

U.O. Chirurgia Plastica, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Gian L Gatti (GL)

U.O. Chirurgia Plastica, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Simone Gana (S)

Sezione Genetica Medica, Medicina Interna 1, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Maria A Caligo (MA)

SOD Genetica Molecolare, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Silvano Bertelloni (S)

Pediatric Division, Department of Obstetrics, Gynecology and Pediatrics, Azienda Ospedaliero-Universitaria Pisana, Pisa, Italy.

Classifications MeSH