Investigating the Protein Signature of Adamantinomatous Craniopharyngioma Pediatric Brain Tumor Tissue: Towards the Comprehension of Its Aggressive Behavior.


Journal

Disease markers
ISSN: 1875-8630
Titre abrégé: Dis Markers
Pays: United States
ID NLM: 8604127

Informations de publication

Date de publication:
2019
Historique:
received: 20 12 2018
revised: 14 03 2019
accepted: 31 03 2019
entrez: 14 6 2019
pubmed: 14 6 2019
medline: 18 12 2019
Statut: epublish

Résumé

Although histologically benign, adamantinomatous craniopharyngioma (AC) pediatric brain tumor is a locally aggressive disease that frequently determines symptoms and hormonal dysfunctions related to the mass effect on the surrounding structures. Another typical feature of this benign neoplasm is the presence of voluminous liquid cysts frequently associated with the solid component. Even if studies have been devoted to the proteomic characterization of the tumor intracystic fluid, poor explorations have been performed on its solid part, principally investigated by transcriptomics technologies. In the present study, seven specimens of AC whole tumor tissue have been analyzed by LC-MS for a preliminary assessment of the proteomic profile by a top-down/bottom-up integrated approach. Thymosin beta 4, ubiquitin, calmodulin, S100 proteins, prothymosin

Identifiants

pubmed: 31191748
doi: 10.1155/2019/3609789
pmc: PMC6525946
doi:

Substances chimiques

Biomarkers, Tumor 0
Proteome 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

3609789

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Auteurs

Claudia Martelli (C)

Istituto di Biochimica e Biochimica Clinica, Università Cattolica del Sacro Cuore, Roma, Italy.

Riccardo Serra (R)

Università Cattolica del Sacro Cuore, Istituto di Neurochirurgia, Roma, Italy.

Ilaria Inserra (I)

Istituto di Biochimica e Biochimica Clinica, Università Cattolica del Sacro Cuore, Roma, Italy.

Diana Valeria Rossetti (DV)

Istituto di Biochimica e Biochimica Clinica, Università Cattolica del Sacro Cuore, Roma, Italy.
Fondazione Policlinico Universitario A. Gemelli IRCCS, Roma, Italy.

Federica Iavarone (F)

Istituto di Biochimica e Biochimica Clinica, Università Cattolica del Sacro Cuore, Roma, Italy.
Fondazione Policlinico Universitario A. Gemelli IRCCS, Roma, Italy.

Federica Vincenzoni (F)

Istituto di Biochimica e Biochimica Clinica, Università Cattolica del Sacro Cuore, Roma, Italy.
Fondazione Policlinico Universitario A. Gemelli IRCCS, Roma, Italy.

Massimo Castagnola (M)

Istituto di Chimica del Riconoscimento Molecolare, Consiglio Nazionale delle Ricerche, Roma, Italy.
Laboratorio di Proteomica e Metabonomica, IRCCS-Fondazione Santa Lucia, Roma, Italy.

Andrea Urbani (A)

Istituto di Biochimica e Biochimica Clinica, Università Cattolica del Sacro Cuore, Roma, Italy.
Area Diagnostica di Laboratorio, Fondazione Policlinico Universitario Agostino Gemelli-IRCCS, Roma, Italy.

Gianpiero Tamburrini (G)

Università Cattolica del Sacro Cuore, Istituto di Neurochirurgia, Roma, Italy.
Fondazione Policlinico Universitario A. Gemelli IRCCS, Neurochirurgia Pediatrica, Roma, Italy.

Massimo Caldarelli (M)

Università Cattolica del Sacro Cuore, Istituto di Neurochirurgia, Roma, Italy.
Fondazione Policlinico Universitario A. Gemelli IRCCS, Neurochirurgia Pediatrica, Roma, Italy.

Luca Massimi (L)

Università Cattolica del Sacro Cuore, Istituto di Neurochirurgia, Roma, Italy.
Fondazione Policlinico Universitario A. Gemelli IRCCS, Neurochirurgia Pediatrica, Roma, Italy.

Claudia Desiderio (C)

Istituto di Chimica del Riconoscimento Molecolare, Consiglio Nazionale delle Ricerche, Roma, Italy.

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Classifications MeSH