Phenotypic Overlap of Roberts and Baller-Gerold Syndromes in Two Patients With Craniosynostosis, Limb Reductions, and

Baller-Gerold syndrome ESCO2 RECQL4 Roberts syndrome differential diagnosis genetic counseling patient management

Journal

Frontiers in pediatrics
ISSN: 2296-2360
Titre abrégé: Front Pediatr
Pays: Switzerland
ID NLM: 101615492

Informations de publication

Date de publication:
2019
Historique:
received: 22 11 2018
accepted: 08 05 2019
entrez: 14 6 2019
pubmed: 14 6 2019
medline: 14 6 2019
Statut: epublish

Résumé

Baller-Gerold (BGS, MIM#218600) and Roberts (RBS, MIM#268300) syndromes are rare autosomal recessive disorders caused, respectively, by biallelic alterations in

Identifiants

pubmed: 31192177
doi: 10.3389/fped.2019.00210
pmc: PMC6546804
doi:

Types de publication

Case Reports

Langues

eng

Pagination

210

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Auteurs

Elisa Adele Colombo (EA)

Genetica Medica, Dipartimento di Scienze della Salute, Università degli Studi di Milano, Milan, Italy.

Hatice Mutlu-Albayrak (H)

Department of Pediatric Genetics, Cengiz Gökcek Maternity and Children's Hospital, Gaziantep, Turkey.

Yousef Shafeghati (Y)

Sarem Cell Research Center and Medical Genetics Department, Sarem Women Hospital, Tehran, Iran.

Mine Balasar (M)

Department of Medical Genetics, Meram Medical Faculty, Necmettin Erbakan University, Konya, Turkey.

Juliette Piard (J)

Centre de génétique humaine CHU, Université de Franche-Comté, Besançon, France.

Davide Gentilini (D)

Laboratorio di Biologia Molecolare, Istituto Auxologico Italiano, IRCCS, Milan, Italy.
Department of Brain and Behavioral Sciences, University of Pavia, Pavia, Italy.

Anna Maria Di Blasio (AM)

Laboratorio di Biologia Molecolare, Istituto Auxologico Italiano, IRCCS, Milan, Italy.

Cristina Gervasini (C)

Genetica Medica, Dipartimento di Scienze della Salute, Università degli Studi di Milano, Milan, Italy.

Lionel Van Maldergem (L)

Centre de génétique humaine CHU, Université de Franche-Comté, Besançon, France.

Lidia Larizza (L)

Laboratorio di Citogenetica e Genetica Molecolare Umana, Istituto Auxologico Italiano, IRCCS, Milan, Italy.

Classifications MeSH