Acquired platelet dysfunction and overproduction of platelet cyclic AMP in two patients with myeloid malignancies.
Blood Platelet Disorders
Myelodysplastic Syndrome (MDS)
Myeloid Leukemia
Platelet Function Tests
cyclic AMP
Journal
Platelets
ISSN: 1369-1635
Titre abrégé: Platelets
Pays: England
ID NLM: 9208117
Informations de publication
Date de publication:
2019
2019
Historique:
pubmed:
27
6
2019
medline:
8
2
2020
entrez:
27
6
2019
Statut:
ppublish
Résumé
The pathophysiology of impaired platelet function in acquired disorders is often poorly understood. We report two unrelated patients with hematologic malignancies associated with acquired severe bleeding diathesis, and complex platelet function abnormalities, including overproduction of the physiological inhibitor cyclic-AMP (cAMP). Patient 1, with mild macrocytic anemia and thrombocytopenia (100 x 10
Identifiants
pubmed: 31240986
doi: 10.1080/09537104.2019.1636020
doi:
Substances chimiques
Cyclic AMP
E0399OZS9N
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM