Management of Chronic Respiratory Failure in Interstitial Lung Diseases: Overview and Clinical Insights.


Journal

International journal of medical sciences
ISSN: 1449-1907
Titre abrégé: Int J Med Sci
Pays: Australia
ID NLM: 101213954

Informations de publication

Date de publication:
2019
Historique:
received: 02 01 2019
accepted: 05 05 2019
entrez: 26 7 2019
pubmed: 26 7 2019
medline: 15 2 2020
Statut: epublish

Résumé

Interstitial lung diseases (ILDs) may be complicated by chronic respiratory failure (CRF), especially in the advanced stages. Aim of this narrative review is to evaluate the current evidence in management of CRF in ILDs. Many physiological mechanisms underlie CRF in ILDs, including lung restriction, ventilation/perfusion mismatch, impaired diffusion capacity and pulmonary vascular damage. Intermittent exertional hypoxemia is often the initial sign of CRF, evolving, as ILD progresses, into continuous hypoxemia. In the majority of the cases, the development of CRF is secondary to the worsening of the underlying disease; however, associated comorbidities may also play a role. When managing CRF in ILDs, the need for pulmonary rehabilitation, the referral to lung transplant centers and palliative care should be assessed and, if necessary, promptly offered. Long-term oxygen therapy is commonly prescribed in case of resting or exertional hypoxemia with the purpose to decrease dyspnea and improve exercise tolerance. High-Flow Nasal Cannula oxygen therapy may be used as an alternative to conventional oxygen therapy for ILD patients with severe hypoxemia requiring both high flows and high oxygen concentrations. Non-Invasive Ventilation may be used in the chronic setting for palliation of end-stage ILD patients, although the evidence to support this application is very limited.

Identifiants

pubmed: 31341410
doi: 10.7150/ijms.32752
pii: ijmsv16p0967
pmc: PMC6643124
doi:

Substances chimiques

Oxygen S88TT14065

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

967-980

Déclaration de conflit d'intérêts

Competing Interests: The authors have declared that no competing interest exists.

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Auteurs

Paola Faverio (P)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Federica De Giacomi (F)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Giulia Bonaiti (G)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Anna Stainer (A)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Luca Sardella (L)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Giulia Pellegrino (G)

Casa di Cura del Policlinico, Dipartimento di Scienze Neuroriabilitative, Milan, Italy.

Giuseppe Francesco Sferrazza Papa (GF)

Casa di Cura del Policlinico, Dipartimento di Scienze Neuroriabilitative, Milan, Italy.

Francesco Bini (F)

UOC Pulmonology, Department of Internal Medicine, Ospedale ASST-Rhodense, Garbagnate Milanese, Italy.

Bruno Dino Bodini (BD)

Pulmonology Unit, Ospedale Maggiore della Carità, University of Piemonte Orientale, Novara, Italy.

Mauro Carone (M)

UOC Pulmonology and Pulmonary Rehabilitation, Istituti Clinici Scientifici Maugeri, IRCCS di Cassano Murge (BA), Italy.

Sara Annoni (S)

Physical therapy and Rehabilitation Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Grazia Messinesi (G)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

Alberto Pesci (A)

School of Medicine and Surgery, University of Milano-Bicocca, Monza, Italy; Respiratory Unit, San Gerardo Hospital, ASST di Monza, Monza, Italy.

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