The Osteocyte Transcriptome Is Extensively Dysregulated in Mouse Models of Osteogenesis Imperfecta.
COLLAGEN
GENETIC ANIMAL MODELS
OSTEOCYTES
OSTEOGENESIS IMPERFECTA
RNASEQ
Journal
JBMR plus
ISSN: 2473-4039
Titre abrégé: JBMR Plus
Pays: England
ID NLM: 101707013
Informations de publication
Date de publication:
Jul 2019
Jul 2019
Historique:
received:
14
11
2018
revised:
19
12
2018
accepted:
13
01
2019
entrez:
3
8
2019
pubmed:
3
8
2019
medline:
3
8
2019
Statut:
epublish
Résumé
Osteocytes are long-lived, highly interconnected, terminally differentiated osteoblasts that reside within mineralized bone matrix. They constitute about 95% of adult bone cells and play important functions including in the regulation of bone remodeling, phosphate homeostasis, and mechanical stimuli sensing and response. However, the role of osteocytes in the pathogenesis of congenital diseases of abnormal bone matrix is poorly understood. This study characterized in vivo transcriptional changes in osteocytes from
Identifiants
pubmed: 31372585
doi: 10.1002/jbm4.10171
pii: JBM410171
pmc: PMC6659450
doi:
Types de publication
Journal Article
Langues
eng
Pagination
e10171Subventions
Organisme : NIGMS NIH HHS
ID : P20 GM125503
Pays : United States
Organisme : NIAMS NIH HHS
ID : R01 AR060823
Pays : United States
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