CPVT: Arrhythmogenesis, Therapeutic Management, and Future Perspectives. A Brief Review of the Literature.
CPVT
arrhythmias
channelopathies
genes
risk stratification
sudden death
Journal
Frontiers in cardiovascular medicine
ISSN: 2297-055X
Titre abrégé: Front Cardiovasc Med
Pays: Switzerland
ID NLM: 101653388
Informations de publication
Date de publication:
2019
2019
Historique:
received:
16
01
2019
accepted:
21
06
2019
entrez:
6
8
2019
pubmed:
6
8
2019
medline:
6
8
2019
Statut:
epublish
Résumé
Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a primary electrical disease characterized by a normal resting electrocardiogram and induction of malignant arrhythmias during adrenergic stress leading to syncope or sudden cardiac death (SCD). CPVT is caused by mutations in the cardiac ryanodine receptor (RyR2) or in the sarcoplasmic reticulum protein calsequestrin 2 genes (
Identifiants
pubmed: 31380394
doi: 10.3389/fcvm.2019.00092
pmc: PMC6644488
doi:
Types de publication
Journal Article
Review
Langues
eng
Pagination
92Références
J Am Coll Cardiol. 1999 Dec;34(7):2035-42
pubmed: 10588221
Circulation. 2001 Jun 12;103(23):2822-7
pubmed: 11401939
J Am Coll Cardiol. 2002 Jul 17;40(2):341-9
pubmed: 12106942
Heart. 2003 Jan;89(1):66-70
pubmed: 12482795
J Clin Invest. 2005 Aug;115(8):2033-8
pubmed: 16075044
J Med Genet. 2005 Nov;42(11):863-70
pubmed: 16272262
Int Heart J. 2006 May;47(3):381-9
pubmed: 16823244
Cardiovasc Res. 2008 Jan 15;77(2):274-84
pubmed: 18006441
Circ Res. 2008 Aug 1;103(3):298-306
pubmed: 18583715
Prog Cardiovasc Dis. 2008 Jul-Aug;51(1):23-30
pubmed: 18634915
J Mol Cell Cardiol. 2009 Feb;46(2):149-59
pubmed: 19027025
Circulation. 2009 May 12;119(18):2426-34
pubmed: 19398665
J Mol Cell Cardiol. 2010 Feb;48(2):293-301
pubmed: 19835880
Europace. 2010 Mar;12(3):417-23
pubmed: 20106799
J Am Coll Cardiol. 2011 May 31;57(22):2244-54
pubmed: 21616285
Circ Res. 2011 Jul 22;109(3):291-5
pubmed: 21680895
Heart Rhythm. 2013 Apr;10(4):542-7
pubmed: 23286974
Europace. 2013 Oct;15(10):1389-406
pubmed: 23994779
J Thorac Cardiovasc Surg. 2014 Jan;147(1):404-9
pubmed: 24268954
Neth Heart J. 2014 Apr;22(4):160-6
pubmed: 24522951
Ann Noninvasive Electrocardiol. 2014 Jul;19(4):311-8
pubmed: 25040480
J Am Coll Cardiol. 2015 Mar 10;65(9):879-88
pubmed: 25744005
Circulation. 2015 Jun 23;131(25):2185-93
pubmed: 26019152
Circulation. 2016 Jun 14;133(24):2348-59
pubmed: 27169737
JACC Basic Transl Sci. 2016 Jun;1(4):251-266
pubmed: 27747307
J Arrhythm. 2016 Oct;32(5):344-351
pubmed: 27761157
Curr Opin Cardiol. 2017 Jan;32(1):78-85
pubmed: 27861184
Biology (Basel). 2017 Jan 29;6(1):null
pubmed: 28146053
Heart Rhythm. 2017 Jul;14(7):1053-1060
pubmed: 28336343
JAMA Cardiol. 2017 Jul 1;2(7):759-766
pubmed: 28492868
J Am Coll Cardiol. 2018 May 1;71(17):1897-1906
pubmed: 29699616