Massive recurrent post-tonsillectomy bleedings revealing a transient factor XIII deficiency in a 10-year-old boy. A case report.

Bleeding Management Tonsillectomy Transient factor XIII deficiency

Journal

International journal of pediatrics & adolescent medicine
ISSN: 2352-6467
Titre abrégé: Int J Pediatr Adolesc Med
Pays: Netherlands
ID NLM: 101670718

Informations de publication

Date de publication:
Jun 2019
Historique:
received: 04 02 2019
revised: 10 04 2019
accepted: 26 05 2019
entrez: 8 8 2019
pubmed: 8 8 2019
medline: 8 8 2019
Statut: ppublish

Résumé

A previously healthy 10-year-old boy was hospitalized for a left cervical abscess associated with massive tonsillar hypertrophy. He underwent abscess drainage and bilateral tonsillectomy. At H36 post-surgery, he presented with tonsillar hemorrhage requiring surgical revision. Hemorrhage relapsed 2 days later, with a total of 7 episodes, 5 of which required surgical revisions. Laboratory investigations were normal except for a markedly low factor XIII (FXIII) activity at 7%. After administration of a single dose of 40 IU/kg plasma-derived FXIII (Fibrogammin

Identifiants

pubmed: 31388547
doi: 10.1016/j.ijpam.2019.05.006
pii: S2352-6467(19)30011-0
pmc: PMC6676365
doi:

Types de publication

Case Reports

Langues

eng

Pagination

55-57

Commentaires et corrections

Type : ErratumIn

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Auteurs

M Jankovic (M)

Pediatrics & Neonatal Medicine Department, Switzerland.

M L Choucair (ML)

Pediatrics & Neonatal Medicine Department, Switzerland.

B Hallak (B)

ENT Department - Centre Hospitalier du Valais Romand, Sion, Switzerland.

E Hernandez (E)

Pediatrics & Neonatal Medicine Department, Switzerland.

M Russo (M)

Pediatrics & Neonatal Medicine Department, Switzerland.

J Llor (J)

Pediatrics & Neonatal Medicine Department, Switzerland.

S Kayemba-Kay's (S)

Pediatrics & Neonatal Medicine Department, Switzerland.

Classifications MeSH