Prognostic Factors in Anti-glomerular Basement Membrane Disease: A Multicenter Study of 119 Patients.


Journal

Frontiers in immunology
ISSN: 1664-3224
Titre abrégé: Front Immunol
Pays: Switzerland
ID NLM: 101560960

Informations de publication

Date de publication:
2019
Historique:
received: 19 12 2018
accepted: 03 07 2019
entrez: 10 8 2019
pubmed: 10 8 2019
medline: 21 10 2020
Statut: epublish

Résumé

We report the overall and renal outcome in a French nationwide multicenter cohort of 119 patients with anti-glomerular basement membrane (anti-GBM) disease. Sixty-four patients (54%) had an exclusive renal involvement, 7 (6%) an isolated alveolar hemorrhage and 48 (40%) a combined renal and pulmonary involvement. Initial renal replacement therapy (RRT) was required in 78% of patients; 82% received plasmapheresis, 82% cyclophosphamide, and 9% rituximab. ANCA positive (28%) patients were older (70 vs. 47 years,

Identifiants

pubmed: 31396214
doi: 10.3389/fimmu.2019.01665
pmc: PMC6662558
doi:

Types de publication

Journal Article Multicenter Study

Langues

eng

Sous-ensembles de citation

IM

Pagination

1665

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Auteurs

Cindy Marques (C)

Inflammation-Immunopathology-Biotherapy Department (DHU i2B), Sorbonne Université, UPMC Univ Paris 06, UMR 7211, Paris, France.
INSERM, UMR_S 959, Paris, France.
CNRS, FRE3632, Paris, France.
AP-HP, Groupe Hospitalier Pitié-Salpêtrière, Department of Internal Medicine and Clinical Immunology, Paris, France.
Centre de Référence des Maladies Auto-Immunes et Systémiques Rares, Centre de Référence des Maladies Auto-Inflammatoires et de l'Amylose, Paris, France.

Julien Carvelli (J)

Aix-Marseille Univ, APHM, C2VN, INRA 1260, INSERM 1263, CHU de la Conception, Centre de Néphrologie et Transplantation Rénale, Marseille, France.

Lucie Biard (L)

Department of Biostatistics and Medical Information, INSERM UMR1153 ECSTRRA Team, Hôpital Saint Louis, AP-HP, Paris, France.

Stanislas Faguer (S)

Département de Néphrologie et Transplantation d'organes, Centre de référence des maladies rénales rares, Hôpital Rangueil, CHU de Toulouse, Toulouse, France.

François Provôt (F)

Department of Nephrology, Centre Hospitalier Régional Universitaire de Lille, Lille, France.

Marie Matignon (M)

Department of Nephrology and Renal Transplantation, Groupe Hospitalier Henri-Mondor, AP-HP, Créteil, France.

Jean-Jacques Boffa (JJ)

Sorbonne Université, UPMC Université Paris 06, Hôpital Tenon, Urgences Néphrologiques et Transplantation Rénale, Paris, France.

Emmanuelle Plaisier (E)

Sorbonne Université, UPMC Université Paris 06, Hôpital Tenon, Urgences Néphrologiques et Transplantation Rénale, Paris, France.

Alexandre Hertig (A)

Sorbonne Université, UPMC Université Paris 06, Hôpital Tenon, Urgences Néphrologiques et Transplantation Rénale, Paris, France.

Maxime Touzot (M)

AURA Paris Plaisance, Paris, France.

Olivier Moranne (O)

Service Néphrologie-Dialyses-Aphérèse, Hôpital Caremeau, CHU Nîmes, et Faculté de Médecine Université de Montpellier-nimes, Nîmes, France.

Xavier Belenfant (X)

Nephrology and Dialysis, Centre Hospitalier Intercommunal André Grégoire, Montreuil, France.

Djillali Annane (D)

General ICU, Hôpital Raymond Poincaré, AP-HP, Garches, France.

Thomas Quéméneur (T)

Department of Internal Medicine, Centre Hospitalier, Valenciennes, France.

Jacques Cadranel (J)

Chest Department and Constitutive Center for Rare Pulmonary Disease, Hôpital Tenon, AP-HP; Inflammation-Immunopathology-Biotherapy Department (DHU i2B) and Sorbonne Université, Paris, France.

Hassan Izzedine (H)

Department of Nephrology, Peupliers Private Hospital, Ramsay Générale de Santé, Paris, France.

Nicolas Bréchot (N)

Medical-Surgical Intensive Care Unit, AP-HP, Groupe Hospitalier Pitié-Salpêtrière, Paris, France.

Patrice Cacoub (P)

Inflammation-Immunopathology-Biotherapy Department (DHU i2B), Sorbonne Université, UPMC Univ Paris 06, UMR 7211, Paris, France.
INSERM, UMR_S 959, Paris, France.
CNRS, FRE3632, Paris, France.
AP-HP, Groupe Hospitalier Pitié-Salpêtrière, Department of Internal Medicine and Clinical Immunology, Paris, France.
Centre de Référence des Maladies Auto-Immunes et Systémiques Rares, Centre de Référence des Maladies Auto-Inflammatoires et de l'Amylose, Paris, France.

Alexis Piedrafita (A)

Département de Néphrologie et Transplantation d'organes, Centre de référence des maladies rénales rares, Hôpital Rangueil, CHU de Toulouse, Toulouse, France.

Noémie Jourde-Chiche (N)

Aix-Marseille Univ, APHM, C2VN, INRA 1260, INSERM 1263, CHU de la Conception, Centre de Néphrologie et Transplantation Rénale, Marseille, France.

David Saadoun (D)

Inflammation-Immunopathology-Biotherapy Department (DHU i2B), Sorbonne Université, UPMC Univ Paris 06, UMR 7211, Paris, France.
INSERM, UMR_S 959, Paris, France.
CNRS, FRE3632, Paris, France.
AP-HP, Groupe Hospitalier Pitié-Salpêtrière, Department of Internal Medicine and Clinical Immunology, Paris, France.
Centre de Référence des Maladies Auto-Immunes et Systémiques Rares, Centre de Référence des Maladies Auto-Inflammatoires et de l'Amylose, Paris, France.

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Classifications MeSH