Esophageal carcinoma cuniculatum: systematic review of the literature and report of two cases.


Journal

Pathology, research and practice
ISSN: 1618-0631
Titre abrégé: Pathol Res Pract
Pays: Germany
ID NLM: 7806109

Informations de publication

Date de publication:
Oct 2019
Historique:
received: 24 06 2019
revised: 31 07 2019
accepted: 16 08 2019
pubmed: 2 9 2019
medline: 28 2 2020
entrez: 2 9 2019
Statut: ppublish

Résumé

Carcinoma cuniculatum (CC) is a rare variant of an extremely well-differentiated squamous cell carcinoma. The most commonly involved site is the skin, with a preference for the sole. Only 15 cases of esophageal CC have been reported so far. Based on published data, the clinical behavior of CC has not been clearly defined. We describe the clinical-pathologic features of two cases of esophageal CC, and provide a review of the available literature, to shed more light on this unusual tumor. A detailed gross and histologic analysis was performed on two cases of surgically treated esophageal CC. The patients were followed-up after surgery. A systematic search was also done concerning studies focused on esophageal CC. A search of the electronic databases MEDLINE-PubMed was conducted using the following research terms: (esophagus) AND (cuniculatum carcinoma). Both patients were alive at last follow-up at six and nine months from surgery without any recurrence. Concerning the fifteen cases reported from the systematic review, median follow-up after surgery was very long as compared to common esophageal cancers (4.0 years), with only one recurrence observed. CC shows an indolent clinical behavior, with a low recurrence rate after radical surgery. The diagnosis of this rare tumor is typically made after surgery. An aggressive approach is required with curative intents.

Sections du résumé

BACKGROUND AND AIMS OBJECTIVE
Carcinoma cuniculatum (CC) is a rare variant of an extremely well-differentiated squamous cell carcinoma. The most commonly involved site is the skin, with a preference for the sole. Only 15 cases of esophageal CC have been reported so far. Based on published data, the clinical behavior of CC has not been clearly defined. We describe the clinical-pathologic features of two cases of esophageal CC, and provide a review of the available literature, to shed more light on this unusual tumor.
METHODS METHODS
A detailed gross and histologic analysis was performed on two cases of surgically treated esophageal CC. The patients were followed-up after surgery. A systematic search was also done concerning studies focused on esophageal CC. A search of the electronic databases MEDLINE-PubMed was conducted using the following research terms: (esophagus) AND (cuniculatum carcinoma).
RESULTS RESULTS
Both patients were alive at last follow-up at six and nine months from surgery without any recurrence. Concerning the fifteen cases reported from the systematic review, median follow-up after surgery was very long as compared to common esophageal cancers (4.0 years), with only one recurrence observed.
CONCLUSION CONCLUSIONS
CC shows an indolent clinical behavior, with a low recurrence rate after radical surgery. The diagnosis of this rare tumor is typically made after surgery. An aggressive approach is required with curative intents.

Identifiants

pubmed: 31472995
pii: S0344-0338(19)31274-9
doi: 10.1016/j.prp.2019.152602
pii:
doi:

Types de publication

Case Reports Journal Article Systematic Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

152602

Informations de copyright

Copyright © 2019 Elsevier GmbH. All rights reserved.

Auteurs

Quirino Lai (Q)

General Surgery and Organ Transplantation Unit, Department of Surgery, Sapienza University of Rome, Italy. Electronic address: lai.quirino@libero.it.

Tiziano de Giacomo (T)

Thoracic Surgery Unit, Department of Surgery, Sapienza University of Rome, Rome, Italy.

Adriano Consolo (A)

General Surgery and Organ Transplantation Unit, Department of Surgery, Sapienza University of Rome, Italy.

Matteo Castrovillari (M)

General Surgery and Organ Transplantation Unit, Department of Surgery, Sapienza University of Rome, Italy.

Fabio Melandro (F)

General Surgery and Organ Transplantation Unit, Department of Surgery, Sapienza University of Rome, Italy.

Bruna Cerbelli (B)

Department of Medico-Surgical Sciences and Biotechnologies, Sapienza University of Rome, Rome, Italy.

Angelina Pernazza (A)

Department of Medico-Surgical Sciences and Biotechnologies, Sapienza University of Rome, Rome, Italy.

Pasquale B Berloco (PB)

General Surgery and Organ Transplantation Unit, Department of Surgery, Sapienza University of Rome, Italy.

Giulia d'Amati (G)

Department of Radiological, Oncological and Pathological Sciences, Sapienza University of Rome, Rome, Italy.

Federico Francioni (F)

Thoracic Surgery Unit, Department of Surgery, Sapienza University of Rome, Rome, Italy.

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Classifications MeSH