FGF23, Hypophosphatemia, and Emerging Treatments.
BUROSUMAB
FGF23
KLOTHO
XLH
X‐LINKED HYPOPHOSPHATEMIA
Journal
JBMR plus
ISSN: 2473-4039
Titre abrégé: JBMR Plus
Pays: England
ID NLM: 101707013
Informations de publication
Date de publication:
Aug 2019
Aug 2019
Historique:
received:
29
12
2018
revised:
13
02
2019
accepted:
26
02
2019
entrez:
6
9
2019
pubmed:
6
9
2019
medline:
6
9
2019
Statut:
epublish
Résumé
FGF23 is an important hormonal regulator of phosphate homeostasis. Together with its co-receptor Klotho, it modulates phosphate reabsorption and both 1α-hydroxylation and 24-hydroxylation in the renal proximal tubules. The most common FGF23-mediated hypophosphatemia is X-linked hypophosphatemia (XLH), caused by mutations in the
Identifiants
pubmed: 31485552
doi: 10.1002/jbm4.10190
pii: JBM410190
pmc: PMC6715782
doi:
Types de publication
Journal Article
Review
Langues
eng
Pagination
e10190Références
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