Development of Murine Systemic Lupus Erythematosus in the Absence of BAFF.


Journal

Arthritis & rheumatology (Hoboken, N.J.)
ISSN: 2326-5205
Titre abrégé: Arthritis Rheumatol
Pays: United States
ID NLM: 101623795

Informations de publication

Date de publication:
02 2020
Historique:
received: 09 01 2019
accepted: 29 08 2019
pubmed: 8 9 2019
medline: 8 5 2020
entrez: 8 9 2019
Statut: ppublish

Résumé

To determine whether systemic lupus erythematosus (SLE) can develop in the absence of BAFF in an SLE-prone host. Starting with C57BL/6 mice that express a human BCL2 transgene (Tg) in their B cells (thereby rendering B cell survival largely independent of BAFF-triggered signals), we introgressed this Tg into NZM 2328 mice genetically deficient in BAFF (NZM.Baff In comparison to their non-Tg NZM.Baff The role of BAFF in the development of SLE-like disease may be dispensable as long as B cell survival is preserved via a BAFF-independent pathway. This may help explain the limited and variable clinical success with BAFF antagonists in human SLE. Thus, NZM.Baff

Identifiants

pubmed: 31493335
doi: 10.1002/art.41097
pmc: PMC6994329
mid: NIHMS1049043
doi:

Substances chimiques

B-Cell Activating Factor 0
Tnfsf13b protein, mouse 0

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

292-302

Subventions

Organisme : NIAMS NIH HHS
ID : R01 AR072212
Pays : United States
Organisme : Alliance for Lupus Research
Pays : International

Informations de copyright

© 2019, American College of Rheumatology.

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Auteurs

William Stohl (W)

University of Southern California Keck School of Medicine, Los Angeles.

Ning Yu (N)

University of Southern California Keck School of Medicine, Los Angeles.

Samantha Chalmers (S)

Albert Einstein College of Medicine, Bronx, New York.

Chaim Putterman (C)

Albert Einstein College of Medicine, Bronx, New York.

Chaim O Jacob (CO)

University of Southern California Keck School of Medicine, Los Angeles.

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Classifications MeSH