Lack of whey acidic protein (WAP) four-disulfide core domain protease inhibitor 2 (WFDC2) causes neonatal death from respiratory failure in mice.
Atelectasis
Cilia
Respiratory disease
Surfactant
Journal
Disease models & mechanisms
ISSN: 1754-8411
Titre abrégé: Dis Model Mech
Pays: England
ID NLM: 101483332
Informations de publication
Date de publication:
12 11 2019
12 11 2019
Historique:
received:
12
04
2019
accepted:
11
09
2019
pubmed:
29
9
2019
medline:
29
5
2020
entrez:
29
9
2019
Statut:
epublish
Résumé
Respiratory failure is a life-threatening problem for pre-term and term infants, yet many causes remain unknown. Here, we present evidence that whey acidic protein (WAP) four-disulfide core domain protease inhibitor 2 (Wfdc2), a protease inhibitor previously unrecognized in respiratory disease, may be a causal factor in infant respiratory failure.
Identifiants
pubmed: 31562139
pii: dmm.040139
doi: 10.1242/dmm.040139
pmc: PMC6899016
pii:
doi:
Substances chimiques
Pulmonary Surfactants
0
WAP Four-Disulfide Core Domain Protein 2
0
Wfdc2 protein, mouse
0
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Informations de copyright
© 2019. Published by The Company of Biologists Ltd.
Déclaration de conflit d'intérêts
Competing interestsThe authors declare no competing or financial interests.
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