Cerebral Amyloid Angiopathy Related Inflammation With Prominent Meningeal Involvement. A Report of 2 Cases.

cerebral amyloid angiopathy (CAA) cerebral amyloid angiopathy-related inflammation (CAA-RI) meningeal inflammation subarachnoid hemorrhage xanthochromia

Journal

Frontiers in neurology
ISSN: 1664-2295
Titre abrégé: Front Neurol
Pays: Switzerland
ID NLM: 101546899

Informations de publication

Date de publication:
2019
Historique:
received: 17 04 2019
accepted: 28 08 2019
entrez: 15 10 2019
pubmed: 15 10 2019
medline: 15 10 2019
Statut: epublish

Résumé

Cerebral amyloid angiopathy related inflammation (CAA-RI) is a rare form of CAA characterized by subacute encephalitic symptoms (cognitive decline, seizures, focal deficits) associated with extensive and confluent white matter lesions co-localizing with lobar microbleeds on brain MRI. We report two cases of unusual CAA-RI mimicking meningoencephalitis but without typical brain lesions on FLAIR and T2

Identifiants

pubmed: 31608002
doi: 10.3389/fneur.2019.00984
pmc: PMC6768005
doi:

Types de publication

Case Reports

Langues

eng

Pagination

984

Informations de copyright

Copyright © 2019 Aghetti, Sène, Polivka, Shor, Lechtman, Chabriat, Jouvent and Guey.

Références

Ann Neurol. 2004 Feb;55(2):250-6
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Neuropathol Appl Neurobiol. 2007 Aug;33(4):475-9
pubmed: 17573809
J Neurol Neurosurg Psychiatry. 2011 Jan;82(1):20-6
pubmed: 20935328
JAMA Neurol. 2016 Feb;73(2):197-202
pubmed: 26720093

Auteurs

Agnès Aghetti (A)

APHP, Lariboisière Hospital, Department of Neurology and DHU NeuroVasc Sorbonne Paris Cité, Paris, France.
INSERM UMR-S 1141, Paris, France.

Damien Sène (D)

Department of Internal Medicine, Lariboisière Hospital, AP-HP, Paris, France.
Univ Paris Diderot, Sorbonne Paris Cité, Paris, France.

Marc Polivka (M)

Department of Pathology, Lariboisière Hospital, AP-HP, Paris, France.

Natalia Shor (N)

Department of Radiology, La Pitié-Salpétrière Hospital, AP-HP, Paris, France.

Sarah Lechtman (S)

Department of Internal Medicine, Lariboisière Hospital, AP-HP, Paris, France.
Univ Paris Diderot, Sorbonne Paris Cité, Paris, France.

Hugues Chabriat (H)

APHP, Lariboisière Hospital, Department of Neurology and DHU NeuroVasc Sorbonne Paris Cité, Paris, France.
INSERM UMR-S 1141, Paris, France.
Univ Paris Diderot, Sorbonne Paris Cité, Paris, France.

Eric Jouvent (E)

APHP, Lariboisière Hospital, Department of Neurology and DHU NeuroVasc Sorbonne Paris Cité, Paris, France.
INSERM UMR-S 1141, Paris, France.
Univ Paris Diderot, Sorbonne Paris Cité, Paris, France.

Stéphanie Guey (S)

APHP, Lariboisière Hospital, Department of Neurology and DHU NeuroVasc Sorbonne Paris Cité, Paris, France.
INSERM UMR-S 1141, Paris, France.
Univ Paris Diderot, Sorbonne Paris Cité, Paris, France.

Classifications MeSH