Auditory EEG Biomarkers in Fragile X Syndrome: Clinical Relevance.
EEG
Fragile X Syndrome
chirp
gamma
habituation
sensory
Journal
Frontiers in integrative neuroscience
ISSN: 1662-5145
Titre abrégé: Front Integr Neurosci
Pays: Switzerland
ID NLM: 101477950
Informations de publication
Date de publication:
2019
2019
Historique:
received:
16
03
2019
accepted:
24
09
2019
entrez:
26
10
2019
pubmed:
28
10
2019
medline:
28
10
2019
Statut:
epublish
Résumé
Sensory hypersensitivities are common and distressing features of Fragile X Syndrome (FXS). While there are many drug interventions that reduce behavioral deficits in Fmr1 mice and efforts to translate these preclinical breakthroughs into clinical trials for FXS, evidence-based clinical interventions are almost non-existent potentially due to lack of valid neural biomarkers. Local circuit function in sensory networks is dependent on the dynamic balance of activity in inhibitory/excitatory synapses. Studies are needed to examine the association of electrophysiological alterations in neural systems with sensory and other clinical features of FXS to establish their clinical relevance. Adolescents and adults with FXS (
Identifiants
pubmed: 31649514
doi: 10.3389/fnint.2019.00060
pmc: PMC6794497
doi:
Types de publication
Journal Article
Langues
eng
Pagination
60Subventions
Organisme : NIMH NIH HHS
ID : K23 MH112936
Pays : United States
Informations de copyright
Copyright © 2019 Ethridge, De Stefano, Schmitt, Woodruff, Brown, Tran, Wang, Pedapati, Erickson and Sweeney.
Références
Am J Occup Ther. 2001 Jan-Feb;55(1):75-82
pubmed: 11216370
Neurobiol Dis. 2016 May;89:126-35
pubmed: 26850918
Biol Psychiatry. 2012 Nov 1;72(9):766-74
pubmed: 22572033
J Neurodev Disord. 2014;6(1):16
pubmed: 26491488
Transl Psychiatry. 2016 Apr 19;6:e787
pubmed: 27093069
Neuroimage. 2015 Nov 15;122:417-26
pubmed: 26216274
Biol Psychol. 2013 Feb;92(2):216-9
pubmed: 23182872
Psychiatry Clin Neurosci. 2015 Oct;69(10):630-9
pubmed: 25854748
J Med Genet. 2008 Aug;45(8):498-9
pubmed: 18413371
Front Cell Neurosci. 2014 Aug 25;8:245
pubmed: 25202236
Neuroreport. 2012 Jan 25;23(2):113-8
pubmed: 22146579
Dev Neurosci. 2011;33(5):337-48
pubmed: 21893938
J Neurodev Disord. 2009 Mar;1(1):91-9
pubmed: 19890439
Front Integr Neurosci. 2019 Jul 25;13:34
pubmed: 31402856
Brain Res. 2013 Apr 19;1506:12-24
pubmed: 23458504
Neuropharmacology. 2013 May;68:83-96
pubmed: 23257237
Psychiatry Res. 2007 Nov 15;156(2):117-27
pubmed: 17913474
J Int Neuropsychol Soc. 2014 Jan;20(1):113-22
pubmed: 24365486
Am J Psychiatry. 2016 Apr 1;173(4):373-84
pubmed: 26651391
Clin Neurophysiol. 2000 Mar;111(3):388-97
pubmed: 10699397
Neurobiol Dis. 2018 Jul;115:39-48
pubmed: 29605426
Nat Rev Drug Discov. 2018 Apr;17(4):280-299
pubmed: 29217836
BMC Psychiatry. 2008 Aug 01;8:66
pubmed: 18673566
J Neurophysiol. 2008 Nov;100(5):2615-26
pubmed: 18784272
J Neurophysiol. 2011 Nov;106(5):2264-72
pubmed: 21795626
Seizure. 2001 Jan;10(1):60-3
pubmed: 11181100
Neurosci Lett. 2008 Mar 28;434(2):218-23
pubmed: 18313850
J Neurodev Disord. 2012 Feb 08;4(1):2
pubmed: 22958782
J Neurodev Disord. 2017 Mar 14;9:11
pubmed: 28316753
Cereb Cortex. 2018 Nov 1;28(11):3951-3964
pubmed: 29040407
J Neurodev Disord. 2017 Jun 12;9:14
pubmed: 28616097
J Neurophysiol. 2002 Jun;87(6):2715-25
pubmed: 12037173
PLoS One. 2014 Jan 22;9(1):e85748
pubmed: 24465679
Curr Biol. 2017 Apr 24;27(8):1111-1123
pubmed: 28366741
Nature. 2009 Jun 4;459(7247):663-7
pubmed: 19396156
Neurobiol Dis. 2019 Apr;124:563-572
pubmed: 30639292
eNeuro. 2017 Mar 1;4(1):
pubmed: 28451631
Trends Cogn Sci. 2010 Nov;14(11):506-15
pubmed: 20932795
J Autism Dev Disord. 2003 Dec;33(6):617-29
pubmed: 14714931
Brain Sci. 2018 Dec 15;8(12):null
pubmed: 30558274
Neuron. 2009 Sep 24;63(6):727-32
pubmed: 19778503
Eur Arch Psychiatry Clin Neurosci. 2015 Sep;265(6):537-40
pubmed: 25182536
J Autism Dev Disord. 2012 Jul;42(7):1377-92
pubmed: 21972117
Eur J Neurosci. 2004 Apr;19(8):2337-44
pubmed: 15090060
Mol Autism. 2017 Jun 7;8:22
pubmed: 28596820
J Autism Dev Disord. 2009 Mar;39(3):495-510
pubmed: 18850262
PLoS One. 2016 Jan 25;11(1):e0147365
pubmed: 26808689
J Neurosci Methods. 2004 Mar 15;134(1):9-21
pubmed: 15102499