Interstitial Lung Disease in Rheumatoid Arthritis Remains a Challenge for Clinicians.
interstitial lung disease
non-specific interstitial pneumonia
organizing pneumonia
rheumatoid arthritis
therapy
usual interstitial pneumonia
Journal
Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588
Informations de publication
Date de publication:
21 Nov 2019
21 Nov 2019
Historique:
received:
27
08
2019
revised:
11
11
2019
accepted:
20
11
2019
entrez:
27
11
2019
pubmed:
27
11
2019
medline:
27
11
2019
Statut:
epublish
Résumé
Interstitial lung disease (ILD) is a serious complication of rheumatoid arthritis (RA) contributing to significantly increased morbidity and mortality. Other respiratory complications, such as chronic obstructive pulmonary disease and bronchiectasis, are frequent in RA. Infections and drug toxicity are important differential diagnoses and should be considered in the diagnostic work-up of patients with RA presenting with respiratory symptoms. This review provides an overview of the epidemiology and pathogenesis of RA-ILD, the radiological and histopathological characteristics of the disease as well as the current and future treatment options. Currently, there is no available evidence-based therapy for RA-ILD, and immunosuppressants are the mainstay of therapy. Ongoing studies are exploring the role of antifibrotic therapy in patients with progressive fibrotic ILD, which may lead to a new treatment approach for subgroups of patients with RA-ILD.
Identifiants
pubmed: 31766446
pii: jcm8122038
doi: 10.3390/jcm8122038
pmc: PMC6947091
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
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