N-acetylcysteine Decreases Fibrosis and Increases Force-Generating Capacity of
DMD
N-acetylcysteine
antioxidant
diaphragm
fibrosis
intercostal
interleukin-1β
interleukin-6
mdx
Journal
Antioxidants (Basel, Switzerland)
ISSN: 2076-3921
Titre abrégé: Antioxidants (Basel)
Pays: Switzerland
ID NLM: 101668981
Informations de publication
Date de publication:
24 Nov 2019
24 Nov 2019
Historique:
received:
30
08
2019
revised:
10
11
2019
accepted:
21
11
2019
entrez:
28
11
2019
pubmed:
28
11
2019
medline:
28
11
2019
Statut:
epublish
Résumé
Respiratory muscle weakness occurs due to dystrophin deficiency in Duchenne muscular dystrophy (DMD). The
Identifiants
pubmed: 31771272
pii: antiox8120581
doi: 10.3390/antiox8120581
pmc: PMC6943616
pii:
doi:
Types de publication
Journal Article
Langues
eng
Subventions
Organisme : The Physiological Society
ID : Research Grant to DE
Déclaration de conflit d'intérêts
The authors declare no conflict of interest.
Références
PLoS One. 2019 Apr 22;14(4):e0215590
pubmed: 31009514
Acta Myol. 2011 Jun;30(1):16-23
pubmed: 21842588
Exp Physiol. 2017 Sep 1;102(9):1177-1193
pubmed: 28665499
Antioxidants (Basel). 2017 Dec 06;6(4):null
pubmed: 29210997
Disabil Rehabil. 2016 Oct;38(20):2052-62
pubmed: 26728920
Int J Exp Pathol. 2015 Oct;96(5):285-93
pubmed: 26515458
Respir Physiol Neurobiol. 2019 Jul;265:49-54
pubmed: 29933052
Respir Physiol Neurobiol. 2016 Jun;226:68-75
pubmed: 26691169
J Physiol. 2019 Feb;597(3):831-848
pubmed: 30570134
Proc Natl Acad Sci U S A. 2015 Oct 13;112(41):12864-9
pubmed: 26417069
Clin Exp Pharmacol Physiol. 2006 Jul;33(7):657-62
pubmed: 16789936
Biol Trace Elem Res. 2015 Sep;167(1):115-20
pubmed: 25762099
Prog Brain Res. 2014;209:309-29
pubmed: 24746055
Cell. 1991 Sep 20;66(6):1121-31
pubmed: 1913804
Curr Neurol Neurosci Rep. 2017 May;17(5):44
pubmed: 28397169
Neurol India. 2008 Jul-Sep;56(3):236-47
pubmed: 18974549
J Physiol. 2017 Dec 1;595(23):7015
pubmed: 29034480
Skelet Muscle. 2015 Jul 15;5:22
pubmed: 26180627
Pediatr Pulmonol. 2015 May;50(5):487-94
pubmed: 25755201
Oxid Med Cell Longev. 2018 Feb 19;2018:4805493
pubmed: 29670681
Adv Exp Med Biol. 2008;605:458-62
pubmed: 18085317
J Muscle Res Cell Motil. 2006;27(1):1-8
pubmed: 16362724
Muscle Nerve. 2012 Nov;46(5):773-84
pubmed: 22847332
J Physiol. 2019 Aug;597(15):4103-4105
pubmed: 31368167
J Muscle Res Cell Motil. 2013 Feb;34(1):1-13
pubmed: 23104273
Am J Respir Crit Care Med. 2000 Jul;162(1):278-81
pubmed: 10903254
Clin Nutr. 2013 Jun;32(3):472-5
pubmed: 22727548
Eur J Neurosci. 2016 Jun;43(12):1623-35
pubmed: 27037492
J Physiol. 2015 Jun 15;593(12):2547-9
pubmed: 26095019
Pediatr Pulmonol. 2014 May;49(5):473-81
pubmed: 23836708
Muscle Nerve. 2017 Dec;56(6):E134-E140
pubmed: 28294390
Compr Physiol. 2013 Oct;3(4):1553-67
pubmed: 24265238
Muscle Nerve. 1987 Feb;10(2):150-4
pubmed: 3821787
Pediatr Neurol. 2007 Jan;36(1):1-7
pubmed: 17162189
Physiol Rep. 2016 Apr;4(7):null
pubmed: 27081162
PLoS One. 2010 Dec 20;5(12):e15354
pubmed: 21187957
J Muscle Res Cell Motil. 2007;28(1):29-37
pubmed: 17431804
J Physiol. 2008 Apr 1;586(7):2003-14
pubmed: 18258657
Front Physiol. 2015 Apr 20;6:122
pubmed: 25941492
J Vasc Surg. 2015 Mar;61(3):777-86
pubmed: 24388697
Int J Chron Obstruct Pulmon Dis. 2006;1(4):425-34
pubmed: 18044098
Am J Physiol Regul Integr Comp Physiol. 2005 Feb;288(2):R345-53
pubmed: 15637171
Am J Pathol. 2010 Sep;177(3):1356-64
pubmed: 20696779
Am J Respir Crit Care Med. 1997 Nov;156(5):1567-71
pubmed: 9372677
Neuromuscul Disord. 2012 May;22(5):427-34
pubmed: 22206641
Thorax. 1994 Feb;49(2):157-61
pubmed: 8128406
Biomed Res Int. 2015;2015:891972
pubmed: 26380303
Eur Respir J. 1994 Aug;7(8):1403-8
pubmed: 7957826
Am J Respir Cell Mol Biol. 2016 Jul;55(1):12-23
pubmed: 26681636
Adv Exp Med Biol. 2015;860:239-44
pubmed: 26303487
Sci Rep. 2017 Dec 18;7(1):17718
pubmed: 29255249
J Paediatr Child Health. 2005 Sep-Oct;41(9-10):500-3
pubmed: 16150067
FASEB J. 2007 Apr;21(4):1210-26
pubmed: 17264171
Muscle Nerve. 2012 Dec;46(6):917-25
pubmed: 23225384
Neuromuscul Disord. 2017 Apr;27(4):307-314
pubmed: 28189481
PLoS One. 2015 Jan 21;10(1):e0117306
pubmed: 25607927
Am J Physiol. 1999 Dec;277(6):C1170-6
pubmed: 10600768
J Physiol. 2018 Feb 15;596(4):737-738
pubmed: 29277904
Free Radic Res. 2011 Sep;45(9):991-9
pubmed: 21696323
Proc Natl Acad Sci U S A. 1993 Apr 15;90(8):3710-4
pubmed: 8475120
Exp Physiol. 2014 Apr;99(4):688-700
pubmed: 24443349
J Neurol Sci. 1984 Mar;63(3):279-83
pubmed: 6726273
Thorax. 1997 May;52(5):472-5
pubmed: 9176541
J Physiol. 2018 Nov;596(21):5175-5197
pubmed: 30160301
Chest. 1989 Dec;96(6):1346-51
pubmed: 2582842
J Physiol. 2017 Nov 1;595(21):6653-6672
pubmed: 28952155
J Appl Physiol (1985). 2003 May;94(5):1744-50
pubmed: 12679345
Pediatr Pulmonol. 2000 Feb;29(2):135-40
pubmed: 10639204
EBioMedicine. 2015 Feb 26;2(4):285-93
pubmed: 26137572
J Appl Physiol (1985). 2001 Feb;90(2):724-31
pubmed: 11160074
Nature. 1991 Aug 8;352(6335):536-9
pubmed: 1865908
Elife. 2018 Jan 30;7:
pubmed: 29381135
Front Physiol. 2015 Sep 09;6:252
pubmed: 26441672
Mol Med. 2011 Sep-Oct;17(9-10):917-24
pubmed: 21607286
J Cell Mol Med. 2006 Jan-Mar;10(1):157-65
pubmed: 16563228
Hum Mol Genet. 2017 Jul 15;26(14):2781-2790
pubmed: 28472288
Hypoxia (Auckl). 2017 Jul 14;5:75-84
pubmed: 28770235
J Physiol. 2011 May 1;589(Pt 9):2161-70
pubmed: 21486793
PLoS One. 2013 Jul 29;8(7):e69567
pubmed: 23922741
Neurochem Res. 2012 Apr;37(4):885-98
pubmed: 22219131
J Physiol. 2017 Dec 1;595(23):7093-7107
pubmed: 28887840
Oxid Med Cell Longev. 2017;2017:1987218
pubmed: 28845212
Am J Pathol. 2006 Apr;168(4):1276-87; quiz 1404-5
pubmed: 16565501