Macular corneal dystrophy with isolated peripheral Descemet membrane deposits.
Corneal dystrophy
Corneal endothelial disease
Macular corneal dystrophy
Journal
American journal of ophthalmology case reports
ISSN: 2451-9936
Titre abrégé: Am J Ophthalmol Case Rep
Pays: United States
ID NLM: 101679941
Informations de publication
Date de publication:
Dec 2019
Dec 2019
Historique:
received:
28
01
2019
revised:
02
09
2019
accepted:
05
11
2019
entrez:
5
12
2019
pubmed:
5
12
2019
medline:
5
12
2019
Statut:
epublish
Résumé
Macular Corneal Dystrophy (MCD, MIM #217800) is a category 1 corneal stromal dystrophy as per the current IC3D classification. While characterized by macular stromal deposits, we report a case of MCD type II with isolated bilateral peripheral Decemet membrane opacities, describing the clinical features and results of screening the A 68-year-old man with an unremarkable past medical and family history presented with bilateral progressive decrease in vision. Ocular exam revealed bilateral clear corneas with the exception of peripheral, round, gray-white discrete deposits at the level of Descemet membrane and decreased central corneal thickness in both eyes. The morphology of the corneal deposits, decreased corneal thickness and the absence of a family history were consistent with MCD, prompting screening of the Although macular corneal dystrophy is classified as a corneal stromal dystrophy with endothelial involvement, we report a case of MCD with dystrophic deposits confined to the peripheral Descemet membrane, indicating that MCD may be associated with isolated endothelial involvement.
Identifiants
pubmed: 31799478
doi: 10.1016/j.ajoc.2019.100571
pii: S2451-9936(19)30013-1
pii: 100571
pmc: PMC6881691
doi:
Types de publication
Case Reports
Langues
eng
Pagination
100571Subventions
Organisme : NEI NIH HHS
ID : P30 EY000331
Pays : United States
Informations de copyright
© 2019 Published by Elsevier Inc.
Déclaration de conflit d'intérêts
All authors have no conflicts of interest to report.
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