Collagen VI Deficiency Results in Structural Abnormalities in the Mouse Lung.
Journal
The American journal of pathology
ISSN: 1525-2191
Titre abrégé: Am J Pathol
Pays: United States
ID NLM: 0370502
Informations de publication
Date de publication:
02 2020
02 2020
Historique:
received:
06
06
2019
revised:
16
09
2019
accepted:
11
10
2019
pubmed:
16
12
2019
medline:
6
5
2020
entrez:
16
12
2019
Statut:
ppublish
Résumé
Collagen VI (COL6) is known for its role in a spectrum of congenital muscular dystrophies, which are often accompanied by respiratory dysfunction. However, little is known regarding the function of COL6 in the lung. We confirmed the presence of COL6 throughout the basement membrane region of mouse lung tissue. Lung structure and organization were studied in a previously described Col6a1
Identifiants
pubmed: 31837950
pii: S0002-9440(19)30851-X
doi: 10.1016/j.ajpath.2019.10.014
pmc: PMC7013274
pii:
doi:
Substances chimiques
Col6a1 protein, mouse
0
Collagen Type VI
0
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
426-441Subventions
Organisme : NIEHS NIH HHS
ID : T32 ES007026
Pays : United States
Organisme : NHLBI NIH HHS
ID : T32 HL066988
Pays : United States
Organisme : NHLBI NIH HHS
ID : U01 HL122700
Pays : United States
Organisme : Howard Hughes Medical Institute
Pays : United States
Informations de copyright
Copyright © 2020 American Society for Investigative Pathology. Published by Elsevier Inc. All rights reserved.
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