Pachydermoperiostosis: A clinicopathological description.
Acromegaloid face
Clubbing
Floppy eyelid syndrome
Pachydermoperiostosis
Journal
Journal of current ophthalmology
ISSN: 2452-2325
Titre abrégé: J Curr Ophthalmol
Pays: India
ID NLM: 101678509
Informations de publication
Date de publication:
Dec 2019
Dec 2019
Historique:
received:
22
11
2018
revised:
24
02
2019
accepted:
04
03
2019
entrez:
18
12
2019
pubmed:
18
12
2019
medline:
18
12
2019
Statut:
epublish
Résumé
To report a case of pachydermoperiostosis (PDP) and a review of the literature. A 32-year-old man was referred to our clinic with bilateral eyelid swelling and blepharoptosis. On examination, marked blepharoptosis was noted, and his eyelids were found to be floppy. Systemic examination was significant for clubbing of digits, coarse acromegalic facial features, and furrowing and oiliness of the skin of scalp and forehead. The patient was diagnosed as a case of PDP. On the brain MRI, the pituitary gland was enlarged, and the border of clivus was irregular. Pituitary and thyroid hormone levels were normal. He underwent bilateral lateral tarsal strip (LTS) procedure to address the eyelid laxity. Histopathologic examination revealed marked sebaceous gland hyperplasia with mucin deposition in the dermis. Floppy eyelid syndrome, clubbing, and acromegaloid face are main features that could lead to the diagnosis of PDP.
Identifiants
pubmed: 31844800
doi: 10.1016/j.joco.2019.03.001
pii: S2452-2325(18)30289-0
pmc: PMC6896461
doi:
Types de publication
Case Reports
Langues
eng
Pagination
450-453Informations de copyright
© 2019 Iranian Society of Ophthalmology. Production and hosting by Elsevier B.V.
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