Selective Neuronal Death in Neurodegenerative Diseases: The Ongoing Mystery.
Striatum
TNTs
cell-to-cell transport
cellular protrusion
mHTT transmission
neuronal death
tissue-specific damage
Journal
The Yale journal of biology and medicine
ISSN: 1551-4056
Titre abrégé: Yale J Biol Med
Pays: United States
ID NLM: 0417414
Informations de publication
Date de publication:
12 2019
12 2019
Historique:
entrez:
24
12
2019
pubmed:
24
12
2019
medline:
25
6
2020
Statut:
epublish
Résumé
A major unresolved problem in neurodegenerative disease is why and how a specific set of neurons in the brain are highly vulnerable to neuronal death. Multiple pathways and mechanisms have been proposed to play a role in Alzheimer disease (AD), Parkinson disease (PD), amyotrophic lateral sclerosis (ALS), and Huntington disease (HD), yet how they contribute to neuronal vulnerability remains far from clear. In this review, various mechanisms ascribed in AD, PD, ALS, and HD will be briefly summarized. Particular focus will be placed on Rhes-mediated intercellular transport of the HD protein and its role in mitophagy, in which I will discuss some intriguing observations that I apply to model striatal vulnerability in HD. I may have unintentionally missed referring some studies in this review, and I extend my apologies to the authors in those circumstances.
Substances chimiques
GTP-Binding Proteins
EC 3.6.1.-
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
695-705Subventions
Organisme : NINDS NIH HHS
ID : R01 NS087019
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS094577
Pays : United States
Informations de copyright
Copyright ©2019, Yale Journal of Biology and Medicine.
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