Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges.
Chiari malformation
Klippel-Trenaunay syndrome
neurosurgery
Journal
Indian journal of anaesthesia
ISSN: 0019-5049
Titre abrégé: Indian J Anaesth
Pays: India
ID NLM: 0013243
Informations de publication
Date de publication:
Dec 2019
Dec 2019
Historique:
received:
28
06
2019
revised:
17
08
2019
accepted:
26
09
2019
entrez:
28
12
2019
pubmed:
28
12
2019
medline:
28
12
2019
Statut:
ppublish
Résumé
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterised by cutaneous capillary malformations, soft tissue and bone hypertrophy and venous varicosities. The coexistence of Chiari 1 malformation and an intracranial tumour has been rarely reported in the literature. Multisystem involvement of this syndrome mandates adequate preparation and planning, with meticulous conduct of anaesthesia to achieve favourable outcomes. We report a case of KTS syndrome with Chiari 1 malformation who had presented for craniotomy, and thereby discuss the challenges faced during anaesthetic management of these patients for major surgeries.
Identifiants
pubmed: 31879429
doi: 10.4103/ija.IJA_510_19
pii: IJA-63-1033
pmc: PMC6921327
doi:
Types de publication
Case Reports
Langues
eng
Pagination
1033-1035Informations de copyright
Copyright: © 2019 Indian Journal of Anaesthesia.
Déclaration de conflit d'intérêts
There are no conflicts of interest.
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