Long-term epilepsy-associated tumors: transcriptional signatures reflect clinical course.


Journal

Scientific reports
ISSN: 2045-2322
Titre abrégé: Sci Rep
Pays: England
ID NLM: 101563288

Informations de publication

Date de publication:
09 01 2020
Historique:
received: 08 01 2019
accepted: 29 11 2019
entrez: 11 1 2020
pubmed: 11 1 2020
medline: 18 11 2020
Statut: epublish

Résumé

Long-term epilepsy-associated tumors (LEATs) represent mostly benign brain tumors associated with drug-resistant epilepsy. The aim of the study was to investigate the specific transcriptional signatures of those tumors and characterize their underlying oncogenic drivers. A cluster analysis of 65 transcriptome profiles from three independent datasets resulted in four distinct transcriptional subgroups. The first subgroup revealed transcriptional activation of STAT3 and TGF-signaling pathways and contained predominantly dysembryoplastic neuroepithelial tumors (DNTs). The second subgroup was characterized by alterations in the MAPK-pathway and up-stream cascades including FGFR and EGFR-mediated signaling. This tumor cluster exclusively contained neoplasms with somatic BRAF

Identifiants

pubmed: 31919458
doi: 10.1038/s41598-019-56146-y
pii: 10.1038/s41598-019-56146-y
pmc: PMC6952384
doi:

Substances chimiques

Biomarkers, Tumor 0

Types de publication

Journal Article Research Support, N.I.H., Extramural

Langues

eng

Sous-ensembles de citation

IM

Pagination

96

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Auteurs

Daniel Delev (D)

Department of Neurosurgery, Medical Center, Freiburg, Germany. daniel.delev@gmail.com.
Department of Neurosurgery, RWTH University Aachen, Aachen, Germany. daniel.delev@gmail.com.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany. daniel.delev@gmail.com.
Medical Faculty, Freiburg University, Freiburg, Germany. daniel.delev@gmail.com.

Karam Daka (K)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Sabrina Heynckes (S)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Annette Gaebelein (A)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Pamela Franco (P)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Dietmar Pfeifer (D)

Department of Hematology, Oncology and Stem Cell Transplantation, Medical Center University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Marco Prinz (M)

Signalling Research Centres BIOSS and CIBSS, University of Freiburg, Freiburg, Germany.
Center for NeuroModulation (NeuroModul), University of Freiburg, Freiburg, Germany.
Institute of Neuropathology, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Oliver Schnell (O)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Horst Urbach (H)

Department of Neuroradiology, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Irina Mader (I)

Department of Neuroradiology, Medical Center, University of Freiburg, Freiburg, Germany.
Clinic for Neuropediatrics and Neurorehabilitation, Epilepsy Center for Children and Adolescents, Schön Klinik, Vogtareuth, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Jürgen Beck (J)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

Alexander Grote (A)

Clinic for Neurosurgery, Evangelic Hospital of Bethel, Bielefeld, Germany.

Albert J Becker (AJ)

Section for Translational Epilepsy Research, Department of Neuropathology, University of Bonn Medical Center, Bonn, Germany.

Dieter Henrik Heiland (DH)

Department of Neurosurgery, Medical Center, Freiburg, Germany.
Translational NeuroOncology Research Group, Medical Center, University of Freiburg, Freiburg, Germany.
Medical Faculty, Freiburg University, Freiburg, Germany.

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