Soft Tissue Special Issue: Adamantinoma-Like Ewing Sarcoma of the Head and Neck: A Practical Review of a Challenging Emerging Entity.
Adamantinoma-like Ewing sarcoma
Complex epithelial differentiation
EWSR1
Ewing sarcoma
FLI1
Journal
Head and neck pathology
ISSN: 1936-0568
Titre abrégé: Head Neck Pathol
Pays: United States
ID NLM: 101304010
Informations de publication
Date de publication:
Mar 2020
Mar 2020
Historique:
received:
16
09
2019
accepted:
12
11
2019
pubmed:
18
1
2020
medline:
20
11
2020
entrez:
18
1
2020
Statut:
ppublish
Résumé
Adamantinoma-like Ewing sarcoma (ALES) is a rare variant of Ewing sarcoma that is defined by complex epithelial differentiation, including expression of cytokeratin and p40 and frequent keratin pearl formation. In recent years, ALES has been increasingly recognized in the head and neck, where it can mimic a wide range of small round blue cell tumors and basaloid carcinomas. However, there has been persistent controversy regarding whether ALES is best classified and managed as a sarcoma or carcinoma. This review summarizes the characteristic clinical, pathologic, immunophenotypic, and molecular features of ALES with an emphasis on differential diagnosis and tumor classification.
Identifiants
pubmed: 31950471
doi: 10.1007/s12105-019-01098-y
pii: 10.1007/s12105-019-01098-y
pmc: PMC7021882
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
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