Bilateral Renal Colic as an Initial Presentation of Erdheim-Chester Disease.
Journal
Case reports in urology
ISSN: 2090-696X
Titre abrégé: Case Rep Urol
Pays: United States
ID NLM: 101580193
Informations de publication
Date de publication:
2019
2019
Historique:
received:
29
10
2019
accepted:
11
12
2019
entrez:
25
1
2020
pubmed:
25
1
2020
medline:
25
1
2020
Statut:
epublish
Résumé
Erdheim-Chester disease (ECD) is a rare non-Langerhans cells histiocytosis characterized by multiorgan involvement, with renal-ECD documented in over one-third of patients. Renal disease is generally asymptomatic, rarely causing hydronephrosis and kidney impairment. In addition, the diverse clinical picture of Erdheim-Chester disease arises slowly with sequential manifestations. We present a rare case of a 75-year-old woman on long-term treatment for panhypopituitarism and steroid therapy for vasculitis, presenting to the emergency department with bilateral renal colic and acute kidney injury. Abdominopelvic CT scan revealed renal infiltration with signs of retroperitoneal fibrosis and hydronephrosis. Kidney CT-guided biopsy and 18-fluorodeoxyglucose (FDG) positron emission tomography whole body scan as well as the history of hypopituitarism and vasculitis confirmed the diagnosis of Erdheim-Chester disease. Proper therapy with interferon-
Identifiants
pubmed: 31976119
doi: 10.1155/2019/4670376
pmc: PMC6953532
doi:
Types de publication
Case Reports
Langues
eng
Pagination
4670376Informations de copyright
Copyright © 2019 Julien Sarkis et al.
Déclaration de conflit d'intérêts
The authors declare that they have no conflict of interest.
Références
Am J Dermatopathol. 2017 Jul;39(7):493-503
pubmed: 27898473
Mayo Clin Proc. 2018 May;93(5):671
pubmed: 29728208
Medicine (Baltimore). 2016 Oct;95(42):e5167
pubmed: 27759649
Case Rep Hematol. 2018 May 16;2018:7865325
pubmed: 29888013
Cancer Res Treat. 2017 Apr;49(2):553-558
pubmed: 27488869
Crit Rev Oncol Hematol. 2015 Jul;95(1):1-11
pubmed: 25744785