Severity of Fontan-Associated Liver Disease Correlates with Fontan Hemodynamics.


Journal

Pediatric cardiology
ISSN: 1432-1971
Titre abrégé: Pediatr Cardiol
Pays: United States
ID NLM: 8003849

Informations de publication

Date de publication:
Apr 2020
Historique:
received: 28 08 2019
accepted: 17 01 2020
pubmed: 2 2 2020
medline: 5 6 2020
entrez: 2 2 2020
Statut: ppublish

Résumé

Fontan-palliated patients are at risk for the development of Fontan-associated liver disease (FALD). In this study, we performed a detailed hemodynamic and hepatic assessment to analyze the incidence and spectrum of FALD and its association with patients' hemodynamics. From 2017 to 2019, 145 patients underwent a detailed, age-adjusted hepatic examination including laboratory analysis (FibroTest

Identifiants

pubmed: 32006084
doi: 10.1007/s00246-020-02291-5
pii: 10.1007/s00246-020-02291-5
pmc: PMC7256101
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

736-746

Subventions

Organisme : Fördergemeinschaft Deutsche Kinderherzzentren
ID : W-B-002/2017

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Auteurs

Anastasia Schleiger (A)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany. schleiger@dhzb.de.

Madeleine Salzmann (M)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany.

Peter Kramer (P)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany.

Friederike Danne (F)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany.

Stephan Schubert (S)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany.

Christian Bassir (C)

Department of Pediatric Radiology, Charité-Universitätsmedizin Berlin, Berlin, Germany.

Tobias Müller (T)

Department of Gastroenterology and Hepatology, Charité Universitätsmedizin Berlin, Berlin, Germany.

Hans-Peter Müller (HP)

Department of Gastroenterology and Hepatology, Charité Universitätsmedizin Berlin, Berlin, Germany.

Felix Berger (F)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany.
DZHK (German Center for Cardiovascular Research), Partner Site Berlin, Berlin, Germany.
Division of Cardiology, Department of Pediatrics, Charité Universitätsmedizin Berlin, Berlin, Germany.

Stanislav Ovroutski (S)

Department of Congenital Heart Disease/Pediatric Cardiology, German Heart Center Berlin, Augustenburger Platz 1, 13353, Berlin, Germany.

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Classifications MeSH