Pregnancy in sickle cell trait: what we do and don't know.
Abortion, Spontaneous
/ etiology
Bacteriuria
/ etiology
Female
Humans
Hypertension, Pregnancy-Induced
/ etiology
Infant, Low Birth Weight
Infant, Newborn
Obstetric Labor, Premature
/ etiology
Pregnancy
Pregnancy Complications
/ etiology
Pregnancy Complications, Hematologic
Pregnancy Outcome
Renal Insufficiency, Chronic
/ etiology
Sickle Cell Trait
/ complications
Venous Thromboembolism
/ etiology
chronic kidney disease
pregnancy
sickle cell trait
venous thromboembolism
Journal
British journal of haematology
ISSN: 1365-2141
Titre abrégé: Br J Haematol
Pays: England
ID NLM: 0372544
Informations de publication
Date de publication:
08 2020
08 2020
Historique:
pubmed:
18
2
2020
medline:
4
3
2021
entrez:
18
2
2020
Statut:
ppublish
Résumé
Sickle cell trait (SCT) is the carrier state for sickle cell disease that results from the HBB rs334 missense mutation (p.Glu6Val) in the β-globin chain of haemoglobin. While not associated with any impact on life expectancy, it has been established that SCT is associated with an increased risk of both venous thromboembolism (and in particular, pulmonary embolism) and chronic kidney disease. It is largely unknown what short- or long-term effect, if any, pregnancy has upon the risk or outcomes of these disorders. In addition, SCT has been linked with various adverse outcomes in pregnancy, ranging from maternal complications such as elevated risk of bacteriuria to potentially life-threatening entities such as pre-eclampsia and prematurity. In these scenarios also, no clear association with SCT has been established. Given the high worldwide prevalence of SCT, further studies addressing these issues are warranted.
Identifiants
pubmed: 32064587
doi: 10.1111/bjh.16518
pmc: PMC7415474
mid: NIHMS1069046
doi:
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
328-335Subventions
Organisme : NHLBI NIH HHS
ID : T32 HL007149
Pays : United States
Organisme : NHLBI NIH HHS
ID : U01 HL117659
Pays : United States
Informations de copyright
© 2020 British Society for Haematology and John Wiley & Sons Ltd.
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